H46-H47
Medium Complexity

Disorders of optic nerve and visual pathways

Primary Specialty: Ophthalmology
Last Updated: 2025-09-09

ICD-10 Codes (107)

80 billable
26 category headers
H47
Other disorders of optic [2nd] nerve and visual pathways
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H47.0
Disorders of optic nerve, not elsewhere classified
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H47.01
Ischemic optic neuropathy
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H47.011
Billable
Ischemic optic neuropathy, right eye
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H47.012
Billable
Ischemic optic neuropathy, left eye
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H47.013
Billable
Ischemic optic neuropathy, bilateral
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H47.019
Billable
Ischemic optic neuropathy, unspecified eye
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H47.02
Hemorrhage in optic nerve sheath
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H47.021
Billable
Hemorrhage in optic nerve sheath, right eye
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H47.022
Billable
Hemorrhage in optic nerve sheath, left eye
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H47.023
Billable
Hemorrhage in optic nerve sheath, bilateral
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H47.029
Billable
Hemorrhage in optic nerve sheath, unspecified eye
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H47.03
Optic nerve hypoplasia
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H47.031
Billable
Optic nerve hypoplasia, right eye
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H47.032
Billable
Optic nerve hypoplasia, left eye
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H47.033
Billable
Optic nerve hypoplasia, bilateral
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H47.039
Billable
Optic nerve hypoplasia, unspecified eye
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H47.09
Other disorders of optic nerve, not elsewhere classified
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H47.091
Billable
Other disorders of optic nerve, not elsewhere classified, right eye
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H47.092
Billable
Other disorders of optic nerve, not elsewhere classified, left eye
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H47.093
Billable
Other disorders of optic nerve, not elsewhere classified, bilateral
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H47.099
Billable
Other disorders of optic nerve, not elsewhere classified, unspecified eye
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H47.1
Papilledema
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H47.10
Billable
Unspecified papilledema
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H47.11
Billable
Papilledema associated with increased intracranial pressure
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H47.12
Billable
Papilledema associated with decreased ocular pressure
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H47.13
Billable
Papilledema associated with retinal disorder
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H47.14
Foster-Kennedy syndrome
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H47.141
Billable
Foster-Kennedy syndrome, right eye
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H47.142
Billable
Foster-Kennedy syndrome, left eye
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H47.143
Billable
Foster-Kennedy syndrome, bilateral
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H47.149
Billable
Foster-Kennedy syndrome, unspecified eye
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H47.2
Optic atrophy
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H47.20
Billable
Unspecified optic atrophy
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H47.21
Primary optic atrophy
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H47.211
Billable
Primary optic atrophy, right eye
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H47.212
Billable
Primary optic atrophy, left eye
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H47.213
Billable
Primary optic atrophy, bilateral
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H47.219
Billable
Primary optic atrophy, unspecified eye
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H47.22
Billable
Hereditary optic atrophy
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H47.23
Glaucomatous optic atrophy
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H47.231
Billable
Glaucomatous optic atrophy, right eye
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H47.232
Billable
Glaucomatous optic atrophy, left eye
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H47.233
Billable
Glaucomatous optic atrophy, bilateral
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H47.239
Billable
Glaucomatous optic atrophy, unspecified eye
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H47.29
Other optic atrophy
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H47.291
Billable
Other optic atrophy, right eye
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H47.292
Billable
Other optic atrophy, left eye
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H47.293
Billable
Other optic atrophy, bilateral
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H47.299
Billable
Other optic atrophy, unspecified eye
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H47.3
Other disorders of optic disc
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H47.31
Coloboma of optic disc
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H47.311
Billable
Coloboma of optic disc, right eye
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H47.312
Billable
Coloboma of optic disc, left eye
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H47.313
Billable
Coloboma of optic disc, bilateral
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H47.319
Billable
Coloboma of optic disc, unspecified eye
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H47.32
Drusen of optic disc
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H47.321
Billable
Drusen of optic disc, right eye
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H47.322
Billable
Drusen of optic disc, left eye
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H47.323
Billable
Drusen of optic disc, bilateral
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H47.329
Billable
Drusen of optic disc, unspecified eye
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H47.33
Pseudopapilledema of optic disc
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H47.331
Billable
Pseudopapilledema of optic disc, right eye
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H47.332
Billable
Pseudopapilledema of optic disc, left eye
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H47.333
Billable
Pseudopapilledema of optic disc, bilateral
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H47.339
Billable
Pseudopapilledema of optic disc, unspecified eye
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H47.39
Other disorders of optic disc
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H47.391
Billable
Other disorders of optic disc, right eye
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H47.392
Billable
Other disorders of optic disc, left eye
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H47.393
Billable
Other disorders of optic disc, bilateral
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H47.399
Billable
Other disorders of optic disc, unspecified eye
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H47.4
Disorders of optic chiasm
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H47.41
Billable
Disorders of optic chiasm in (due to) inflammatory disorders
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H47.42
Billable
Disorders of optic chiasm in (due to) neoplasm
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H47.43
Billable
Disorders of optic chiasm in (due to) vascular disorders
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H47.49
Billable
Disorders of optic chiasm in (due to) other disorders
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H47.5
Disorders of other visual pathways
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H47.51
Disorders of visual pathways in (due to) inflammatory disorders
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H47.511
Billable
Disorders of visual pathways in (due to) inflammatory disorders, right side
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H47.512
Billable
Disorders of visual pathways in (due to) inflammatory disorders, left side
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H47.519
Billable
Disorders of visual pathways in (due to) inflammatory disorders, unspecified side
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H47.52
Disorders of visual pathways in (due to) neoplasm
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H47.521
Billable
Disorders of visual pathways in (due to) neoplasm, right side
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H47.522
Billable
Disorders of visual pathways in (due to) neoplasm, left side
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H47.529
Billable
Disorders of visual pathways in (due to) neoplasm, unspecified side
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H47.53
Disorders of visual pathways in (due to) vascular disorders
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H47.531
Billable
Disorders of visual pathways in (due to) vascular disorders, right side
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H47.532
Billable
Disorders of visual pathways in (due to) vascular disorders, left side
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H47.539
Billable
Disorders of visual pathways in (due to) vascular disorders, unspecified side
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H47.6
Disorders of visual cortex
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H47.61
Cortical blindness
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H47.611
Billable
Cortical blindness, right side of brain
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H47.612
Billable
Cortical blindness, left side of brain
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H47.619
Billable
Cortical blindness, unspecified side of brain
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H47.62
Disorders of visual cortex in (due to) inflammatory disorders
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H47.621
Billable
Disorders of visual cortex in (due to) inflammatory disorders, right side of brain
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H47.622
Billable
Disorders of visual cortex in (due to) inflammatory disorders, left side of brain
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H47.629
Billable
Disorders of visual cortex in (due to) inflammatory disorders, unspecified side of brain
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H47.63
Disorders of visual cortex in (due to) neoplasm
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H47.631
Billable
Disorders of visual cortex in (due to) neoplasm, right side of brain
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H47.632
Billable
Disorders of visual cortex in (due to) neoplasm, left side of brain
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H47.639
Billable
Disorders of visual cortex in (due to) neoplasm, unspecified side of brain
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H47.64
Disorders of visual cortex in (due to) vascular disorders
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H47.641
Billable
Disorders of visual cortex in (due to) vascular disorders, right side of brain
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H47.642
Billable
Disorders of visual cortex in (due to) vascular disorders, left side of brain
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H47.649
Billable
Disorders of visual cortex in (due to) vascular disorders, unspecified side of brain
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H47.9
Billable
Unspecified disorder of visual pathways
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Updates & Changes

FY 2026 Updates

Current Year

Deleted Codes

No codes deleted in this range for FY 2026

No significant changes for FY 2026

This range maintains stability with current coding practices

Historical Changes

  • •FY 2025: Routine maintenance updates with minor terminology clarifications
  • •FY 2024: Enhanced specificity requirements for certain code ranges
  • •FY 2023: Updated documentation guidelines for improved clarity

Upcoming Changes

  • •Proposed updates pending review by Coordination and Maintenance Committee
  • •Under consideration: Enhanced digital health integration codes

Implementation Guidance

  • •Review all FY 2026 updates for H46-H47 codes before implementation
  • •Always verify the most current codes in the ICD-10-CM manual
  • •Ensure clinical documentation supports the selected diagnosis codes
  • +3 more guidance items...

Range Overview

high priority

The ICD-10 code range H46-H47 pertains to disorders of the optic nerve and visual pathways. These codes are used to categorize conditions such as optic neuritis, optic atrophy, and disorders of the visual pathways. The codes in this range are crucial for accurate documentation and billing of these conditions, and are widely used in ophthalmology and neurology specialties.

Key Usage Points:

  • •H46 codes are used for optic neuritis and related conditions.
  • •H47 codes cover a wide range of other disorders of optic nerve and visual pathways.
  • •Always code to the highest level of specificity.
  • •Document the cause of the condition, if known.
  • •Include laterality in the code, if applicable.

Coding Guidelines

When to Use:

  • ✓Patient diagnosed with optic neuritis.
  • ✓Patient suffering from optic atrophy.
  • ✓Patient with a disorder of visual pathways.
  • ✓Patient with glaucomatous optic atrophy.
  • ✓Patient with papilledema.

When NOT to Use:

  • ✗Patient with a general vision problem without a specific diagnosis.
  • ✗Eye infection without optic nerve involvement.
  • ✗Conditions related to the eye but not specifically the optic nerve or visual pathways.
  • ✗Visual disturbances without a diagnosed underlying condition.
  • ✗Patient with macular degeneration.

Code Exclusions

Always verify exclusions with the patient's specific diagnosis and clinical documentation.

Documentation Requirements

Proper documentation for H46-H47 codes should clearly state the specific condition, its cause if known, and the affected side. It should also include any complications or related conditions.

Clinical Information:

  • •Specific diagnosis
  • •Cause of the condition, if known
  • •Affected side (laterality)
  • •Complications or related conditions
  • •Progression of the disease

Supporting Evidence:

  • •Clinical examination findings
  • •Imaging results
  • •Visual field tests
  • •Optic nerve function tests
Good Documentation Example:

Patient diagnosed with left optic neuritis due to multiple sclerosis. Visual field test shows reduced peripheral vision in the left eye.

Poor Documentation Example:

Patient has vision problems.

Common Documentation Errors:

  • âš Not specifying the affected side
  • âš Not including the cause of the condition
  • âš Insufficient detail about the specific condition
  • âš Not documenting related conditions or complications

Range Statistics

Total Codes
80
Billable
Complexity:
Medium
Primary Use:Clinical Documentation
Chapter:

Coding Complexity

Medium
Complexity Rating

The complexity of these codes is medium due to the need for specific diagnoses, the potential for multiple related conditions, and the importance of accurate documentation. Coders must also stay updated on changes to the codes and guidelines.

Key Factors:
  • â–¸Determining the specific condition
  • â–¸Identifying the cause of the condition
  • â–¸Coding for laterality
  • â–¸Documenting related conditions or complications
  • â–¸Keeping up with changes and updates to the codes

Specialty Focus

These codes are primarily used in ophthalmology and neurology, but may also be used in other specialties when a patient's condition involves the optic nerve or visual pathways.

Primary Specialties:
Ophthalmology
60%
Neurology
30%
Clinical Scenarios:
  • • Patient with multiple sclerosis develops optic neuritis.
  • • Patient with glaucoma has glaucomatous optic atrophy.
  • • Patient with a brain tumor has a disorder of the visual pathway.
  • • Patient with hypertension develops papilledema.
  • • Patient with optic atrophy due to unknown cause.

Resources & References

Resources for these codes include the official ICD-10 coding guidelines, clinical reference books, and educational materials from professional coding organizations.

Official Guidelines:

  • ICD-10-CM Official Guidelines for Coding and Reporting
  • American Medical Association ICD-10 resources
  • World Health Organization ICD-10 guide

Clinical References:

  • Clinical Ophthalmology: A Systematic Approach
  • Neurology in Clinical Practice

Educational Materials:

  • American Academy of Professional Coders resources
  • American Health Information Management Association resources

Frequently Asked Questions

Can I use H46-H47 codes for any eye condition?

No, these codes are specifically for disorders of the optic nerve and visual pathways. Other eye conditions have their own codes.