J80-J84
Medium Complexity

Other respiratory diseases principally affecting the interstitium

Primary Specialty: Pulmonology
Last Updated: 2025-09-09

ICD-10 Codes (40)

30 billable
7 category headers
J81
Pulmonary edema
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J81.0
Billable
Acute pulmonary edema
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J81.1
Billable
Chronic pulmonary edema
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J82
Pulmonary eosinophilia, not elsewhere classified
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J82.8
Pulmonary eosinophilia, not elsewhere classified
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J82.81
Billable
Chronic eosinophilic pneumonia
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J82.82
Billable
Acute eosinophilic pneumonia
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J82.83
Billable
Eosinophilic asthma
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J82.89
Billable
Other pulmonary eosinophilia, not elsewhere classified
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J84
Other interstitial pulmonary diseases
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J84.0
Alveolar and parieto-alveolar conditions
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J84.01
Billable
Alveolar proteinosis
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J84.02
Billable
Pulmonary alveolar microlithiasis
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J84.03
Billable
Idiopathic pulmonary hemosiderosis
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J84.09
Billable
Other alveolar and parieto-alveolar conditions
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J84.1
Other interstitial pulmonary diseases with fibrosis
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J84.10
Billable
Pulmonary fibrosis, unspecified
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J84.11
Idiopathic interstitial pneumonia
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J84.111
Billable
Idiopathic interstitial pneumonia, not otherwise specified
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J84.112
Billable
Idiopathic pulmonary fibrosis
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J84.113
Billable
Idiopathic non-specific interstitial pneumonitis
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J84.114
Billable
Acute interstitial pneumonitis
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J84.115
Billable
Respiratory bronchiolitis interstitial lung disease
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J84.116
Billable
Cryptogenic organizing pneumonia
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J84.117
Billable
Desquamative interstitial pneumonia
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J84.17
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
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J84.170
Billable
Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
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J84.178
Billable
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
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J84.2
Billable
Lymphoid interstitial pneumonia
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J84.8
Other specified interstitial pulmonary diseases
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J84.81
Billable
Lymphangioleiomyomatosis
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J84.82
Billable
Adult pulmonary Langerhans cell histiocytosis
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J84.83
Billable
Surfactant mutations of the lung
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J84.84
Other interstitial lung diseases of childhood
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J84.841
Billable
Neuroendocrine cell hyperplasia of infancy
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J84.842
Billable
Pulmonary interstitial glycogenosis
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J84.843
Billable
Alveolar capillary dysplasia with vein misalignment
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J84.848
Billable
Other interstitial lung diseases of childhood
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J84.89
Billable
Other specified interstitial pulmonary diseases
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J84.9
Billable
Interstitial pulmonary disease, unspecified
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Updates & Changes

FY 2026 Updates

Current Year

New Codes (1)

J06.9
Acute upper respiratory infection, unspecified, post-viral syndrome

Revised Codes (2)

J02.9
Acute pharyngitis, unspecified - updated to include rapid strep correlation
J06.0
Acute laryngopharyngitis - enhanced viral etiology specifications

Deleted Codes

No codes deleted in this range for FY 2026

Historical Changes

  • FY 2025: Routine maintenance updates with minor terminology clarifications
  • FY 2024: Enhanced specificity requirements for certain code ranges
  • FY 2023: Updated documentation guidelines for improved clarity

Upcoming Changes

  • Proposed updates pending review by Coordination and Maintenance Committee
  • Under consideration: Enhanced digital health integration codes

Implementation Guidance

  • Review all FY 2026 updates for J80-J84 codes before implementation
  • Always verify the most current codes in the ICD-10-CM manual
  • Ensure clinical documentation supports the selected diagnosis codes
  • +3 more guidance items...

Range Overview

high priority

The J80-J84 range in the ICD-10 covers various respiratory diseases that primarily affect the interstitium, the tissue and space around the air sacs of the lungs. These include conditions like acute respiratory distress syndrome (ARDS), interstitial pneumonia, and pulmonary fibrosis. The codes in this range are used to document these conditions in medical records, insurance claims, and public health research.

Key Usage Points:

  • Always use specific codes that indicate the type of interstitial lung disease.
  • For diseases classified elsewhere, code first the underlying disease.
  • Use additional code, where applicable, to identify exposure to environmental tobacco smoke.
  • Use additional code, where applicable, to identify history of tobacco use.
  • When coding for interstitial emphysema, consider whether it is congenital or not.

Coding Guidelines

When to Use:

  • When a patient presents with symptoms of interstitial lung disease.
  • When a patient is diagnosed with a specific interstitial lung disease.
  • When a patient has a history of interstitial lung disease.
  • When a patient is being treated for interstitial lung disease.
  • When a patient has complications due to interstitial lung disease.

When NOT to Use:

  • When a patient has a respiratory disease that does not primarily affect the interstitium.
  • When a patient has a respiratory disease that is not specified as interstitial.
  • When a patient has a respiratory disease that is classified elsewhere.
  • When a patient has a lung disease that is primarily obstructive, not interstitial.
  • When a patient has a lung disease that is primarily restrictive, not interstitial.

Code Exclusions

Always verify exclusions by consulting the ICD-10 guidelines and the patient's medical history.

Documentation Requirements

Proper documentation for this range should include a clear diagnosis, specifics of the condition, history of the disease, and any relevant complications or comorbidities. It should be based on a thorough medical examination and relevant diagnostic tests.

Clinical Information:

  • Specific diagnosis of the interstitial lung disease
  • Details of the patient's symptoms and clinical findings
  • History of the disease
  • Complications or comorbidities
  • Treatment plan

Supporting Evidence:

  • Results of diagnostic tests
  • Imaging reports
  • Laboratory results
  • Consultation notes
Good Documentation Example:

Patient diagnosed with idiopathic pulmonary fibrosis. Patient presents with shortness of breath and dry cough. CT scan shows honeycombing in both lungs. Patient has a history of smoking.

Poor Documentation Example:

Patient diagnosed with lung disease.

Common Documentation Errors:

  • Not specifying the type of interstitial lung disease
  • Not documenting the patient's history of the disease
  • Not including results of diagnostic tests
  • Not documenting complications or comorbidities

Range Statistics

Total Codes
30
Billable
Complexity:
Medium
Primary Use:Clinical Documentation
Chapter:10

Coding Complexity

Medium
Complexity Rating

The coding complexity for this range is considered medium due to the need for specificity in the diagnosis, the potential for complications or comorbidities, and the variability in treatment plans and patient responses.

Key Factors:
  • Specificity of the diagnosis
  • Presence of complications or comorbidities
  • History of the disease
  • Treatment plan
  • Patient's response to treatment

Specialty Focus

These codes are primarily used by pulmonologists, but may also be used by internists, critical care specialists, and other healthcare providers who treat respiratory diseases.

Primary Specialties:
Pulmonology
70%
Internal Medicine
20%
Critical Care
10%
Clinical Scenarios:
  • A patient with a history of smoking presents with shortness of breath and dry cough.
  • A patient with rheumatoid arthritis develops interstitial lung disease.
  • A patient with idiopathic pulmonary fibrosis is admitted to the ICU for respiratory failure.
  • A patient with interstitial lung disease develops a lung infection.
  • A patient with interstitial lung disease requires long-term oxygen therapy.

Resources & References

Resources for this range include the official ICD-10 guidelines, coding clinics, medical textbooks, and online databases.

Official Guidelines:

  • ICD-10-CM Official Guidelines for Coding and Reporting
  • American Health Information Management Association (AHIMA) Coding Clinic
  • Centers for Disease Control and Prevention (CDC) ICD-10 resources

Clinical References:

  • Harrison's Principles of Internal Medicine
  • UpToDate

Educational Materials:

  • AHIMA ICD-10 training materials
  • American Academy of Professional Coders (AAPC) ICD-10 resources

Frequently Asked Questions

Can I use a J80-J84 code for a patient with a respiratory disease that is not specified as interstitial?

No, the J80-J84 range is specifically for interstitial lung diseases. If the disease is not specified as interstitial, use the appropriate code for the specific condition.