Systemic connective tissue disorders
ICD-10 Codes (92)
M31M31.0M31.1M31.10M31.11M31.19M31.2M31.3M31.30M31.31M31.4M31.5M31.6M31.7M31.8M31.9M32M32.0M32.1M32.10M32.11M32.12M32.13M32.14M32.15M32.19M32.8M32.9M33M33.0M33.00M33.01M33.02M33.03M33.09M33.1M33.10M33.11M33.12M33.13M33.19M33.2M33.20M33.21M33.22M33.29M33.9M33.90M33.91M33.92M33.93M33.99M34M34.0M34.1M34.2M34.8M34.81M34.82M34.83M34.89M34.9M35M35.0M35.00M35.01M35.02M35.03M35.04M35.05M35.06M35.07M35.08M35.09M35.1M35.2M35.3M35.4M35.5M35.6M35.7M35.8M35.81M35.89M35.9M36M36.0M36.1M36.2M36.3M36.4M36.8Updates & Changes
FY 2026 Updates
Deleted Codes
No codes deleted in this range for FY 2026
No significant changes for FY 2026
This range maintains stability with current coding practices
Historical Changes
- •FY 2025: Routine maintenance updates with minor terminology clarifications
- •FY 2024: Enhanced specificity requirements for certain code ranges
- •FY 2023: Updated documentation guidelines for improved clarity
Upcoming Changes
- •Proposed updates pending review by Coordination and Maintenance Committee
- •Under consideration: Enhanced digital health integration codes
Implementation Guidance
- •Review all FY 2026 updates for M30-M36 codes before implementation
- •Always verify the most current codes in the ICD-10-CM manual
- •Ensure clinical documentation supports the selected diagnosis codes
- +3 more guidance items...
Range Overview
The ICD-10 code range M30-M36 pertains to systemic connective tissue disorders. These codes are used to classify a variety of conditions that affect the body's connective tissues, including vasculitis, polymyalgia rheumatica, and systemic lupus erythematosus. The codes are organized by specific disorder, with further subdivisions for manifestations and complications.
Key Usage Points:
- •Always code to the highest level of specificity, considering the type of disorder, the affected body system, and any associated complications.
- •Use additional codes to identify any associated conditions or manifestations not covered by the combination codes.
- •When coding for systemic lupus erythematosus, use M32.9 if no organ or system is involved.
- •For polymyalgia rheumatica, use M35.3. If giant cell arteritis is present, use M31.5 instead.
- •For vasculitis, use M30-M31. The specific code will depend on the type and location of the vasculitis.
Coding Guidelines
When to Use:
- ✓When a patient is diagnosed with a systemic connective tissue disorder.
- ✓When a patient with a known systemic connective tissue disorder presents with a new manifestation or complication.
- ✓When a patient's systemic connective tissue disorder is a significant factor in their current medical management.
- ✓When a patient has a history of a systemic connective tissue disorder that affects their current health status.
When NOT to Use:
- ✗When a patient has a localized connective tissue disorder. Use codes from M00-M25 instead.
- ✗When a patient has a connective tissue disorder that is secondary to another condition. Use the code for the primary condition instead.
- ✗When a patient has a connective tissue disorder that is not systemic. Use the appropriate code from M00-M99.
- ✗When a patient has a history of a systemic connective tissue disorder that does not affect their current health status. Use a code from Z80-Z87 instead.
Code Exclusions
Always verify exclusions in the Tabular List of the ICD-10-CM.
Documentation Requirements
Documentation for systemic connective tissue disorders should include the specific diagnosis, the affected body system(s), and any associated complications or manifestations. If the disorder is a significant factor in the patient's current medical management, this should also be documented.
Clinical Information:
- •Specific diagnosis
- •Affected body system(s)
- •Associated complications or manifestations
- •Impact on current medical management
Supporting Evidence:
- •Clinical notes
- •Laboratory and imaging results
- •Referral letters
- •Hospital admission and discharge summaries
Good Documentation Example:
Patient diagnosed with systemic lupus erythematosus with renal involvement. The disease is currently active and is a significant factor in the patient's medical management.
Poor Documentation Example:
Patient has lupus.
Common Documentation Errors:
- ⚠Not documenting the specific type of disorder
- ⚠Not documenting the affected body system(s)
- ⚠Not documenting associated complications or manifestations
- ⚠Not documenting the impact on current medical management
Range Statistics
Coding Complexity
Coding for systemic connective tissue disorders is of medium complexity due to the need to understand the specific types of disorders, identify the affected body system(s), and recognize associated complications or manifestations. The impact on current medical management must also be considered.
Key Factors:
- ▸Understanding the specific types of systemic connective tissue disorders
- ▸Identifying the affected body system(s)
- ▸Identifying associated complications or manifestations
- ▸Determining the impact on current medical management
Specialty Focus
The M30-M36 range is primarily used by rheumatologists, but may also be used by other specialists such as nephrologists and cardiologists, depending on the affected body system.
Primary Specialties:
Clinical Scenarios:
- • A patient with systemic lupus erythematosus presents with new-onset renal failure.
- • A patient with polymyalgia rheumatica develops giant cell arteritis.
- • A patient with a known systemic connective tissue disorder presents with a new cardiac manifestation.
- • A patient's systemic connective tissue disorder is a significant factor in their current medical management.
- • A patient has a history of a systemic connective tissue disorder that affects their current health status.
Resources & References
Resources for coding systemic connective tissue disorders include the ICD-10-CM Official Guidelines for Coding and Reporting, the American College of Rheumatology's guidelines, and various clinical reference books and online resources.
Official Guidelines:
- ICD-10-CM Official Guidelines for Coding and Reporting
- American College of Rheumatology guidelines
- World Health Organization's International Classification of Diseases
Clinical References:
- Harrison's Principles of Internal Medicine
- UpToDate
Educational Materials:
- American Health Information Management Association (AHIMA) resources
- American Academy of Professional Coders (AAPC) resources
Frequently Asked Questions
Can I use a code from the M30-M36 range for a patient with a localized connective tissue disorder?
No, the M30-M36 range is for systemic connective tissue disorders. For localized connective tissue disorders, use a code from the M00-M25 range.