Q10-Q18
Medium Complexity

Congenital malformations of eye, ear, face and neck

Primary Specialty: Pediatrics
Last Updated: 2025-09-10

ICD-10 Codes (63)

55 billable
0 category headers
Q11
Anophthalmos, microphthalmos and macrophthalmos
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Q11.0
Billable
Cystic eyeball
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Q11.1
Billable
Other anophthalmos
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Q11.2
Billable
Microphthalmos
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Q11.3
Billable
Macrophthalmos
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Q12
Congenital lens malformations
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Q12.0
Billable
Congenital cataract
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Q12.1
Billable
Congenital displaced lens
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Q12.2
Billable
Coloboma of lens
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Q12.3
Billable
Congenital aphakia
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Q12.4
Billable
Spherophakia
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Q12.8
Billable
Other congenital lens malformations
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Q12.9
Billable
Congenital lens malformation, unspecified
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Q13
Congenital malformations of anterior segment of eye
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Q13.0
Billable
Coloboma of iris
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Q13.1
Billable
Absence of iris
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Q13.2
Billable
Other congenital malformations of iris
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Q13.3
Billable
Congenital corneal opacity
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Q13.4
Billable
Other congenital corneal malformations
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Q13.5
Billable
Blue sclera
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Q13.8
Billable
Other congenital malformations of anterior segment of eye
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Q13.81
Billable
Rieger anomaly
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Q13.89
Billable
Other congenital malformations of anterior segment of eye
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Q13.9
Billable
Congenital malformation of anterior segment of eye, unspecified
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Q14
Congenital malformations of posterior segment of eye
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Q14.0
Billable
Congenital malformation of vitreous humor
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Q14.1
Billable
Congenital malformation of retina
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Q14.2
Billable
Congenital malformation of optic disc
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Q14.3
Billable
Congenital malformation of choroid
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Q14.8
Billable
Other congenital malformations of posterior segment of eye
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Q14.9
Billable
Congenital malformation of posterior segment of eye, unspecified
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Q15
Other congenital malformations of eye
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Q15.0
Billable
Congenital glaucoma
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Q15.8
Billable
Other specified congenital malformations of eye
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Q15.9
Billable
Congenital malformation of eye, unspecified
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Q16
Congenital malformations of ear causing impairment of hearing
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Q16.0
Billable
Congenital absence of (ear) auricle
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Q16.1
Billable
Congenital absence, atresia and stricture of auditory canal (external)
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Q16.2
Billable
Absence of eustachian tube
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Q16.3
Billable
Congenital malformation of ear ossicles
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Q16.4
Billable
Other congenital malformations of middle ear
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Q16.5
Billable
Congenital malformation of inner ear
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Q16.9
Billable
Congenital malformation of ear causing impairment of hearing, unspecified
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Q17
Other congenital malformations of ear
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Q17.0
Billable
Accessory auricle
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Q17.1
Billable
Macrotia
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Q17.2
Billable
Microtia
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Q17.3
Billable
Other misshapen ear
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Q17.4
Billable
Misplaced ear
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Q17.5
Billable
Prominent ear
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Q17.8
Billable
Other specified congenital malformations of ear
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Q17.9
Billable
Congenital malformation of ear, unspecified
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Q18
Other congenital malformations of face and neck
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Q18.0
Billable
Sinus, fistula and cyst of branchial cleft
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Q18.1
Billable
Preauricular sinus and cyst
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Q18.2
Billable
Other branchial cleft malformations
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Q18.3
Billable
Webbing of neck
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Q18.4
Billable
Macrostomia
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Q18.5
Billable
Microstomia
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Q18.6
Billable
Macrocheilia
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Q18.7
Billable
Microcheilia
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Q18.8
Billable
Other specified congenital malformations of face and neck
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Q18.9
Billable
Congenital malformation of face and neck, unspecified
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Updates & Changes

FY 2026 Updates

Current Year

New Codes (1)

Q23.4
Hypoplastic left heart syndrome with mitral atresia

Revised Codes (1)

Q21.0
Ventricular septal defect - updated to include hemodynamic significance when known

Deleted Codes

No codes deleted in this range for FY 2026

Historical Changes

  • •FY 2025: Routine maintenance updates with minor terminology clarifications
  • •FY 2024: Enhanced specificity requirements for certain code ranges
  • •FY 2023: Updated documentation guidelines for improved clarity

Upcoming Changes

  • •Proposed updates pending review by Coordination and Maintenance Committee
  • •Under consideration: Enhanced digital health integration codes

Implementation Guidance

  • •Review all FY 2026 updates for Q10-Q18 codes before implementation
  • •Always verify the most current codes in the ICD-10-CM manual
  • •Ensure clinical documentation supports the selected diagnosis codes
  • +3 more guidance items...

Range Overview

high priority

The Q10-Q18 category in ICD-10 represents congenital malformations of the eye, ear, face, and neck. These codes are used to document birth defects and anomalies in these areas, present from birth. This range includes a variety of conditions, from minor malformations to severe deformities, impacting the patient's vision, hearing, facial appearance, and neck function.

Key Usage Points:

  • •Always confirm the specific type of malformation before coding.
  • •Use additional codes to identify any associated conditions or complications.
  • •Understand the difference between malformations (present at birth) and deformities (developed later).
  • •Remember to code for laterality when applicable.
  • •Ensure to document any surgical corrections or ongoing treatments.

Coding Guidelines

When to Use:

  • ✓When a patient presents with a congenital malformation of the eye.
  • ✓When a patient has a congenital malformation of the ear affecting hearing.
  • ✓In cases of congenital facial deformities.
  • ✓When a patient has a congenital malformation of the neck.
  • ✓When documenting a patient's medical history of congenital malformations.

When NOT to Use:

  • ✗When the malformation was not present at birth.
  • ✗When the malformation is not in the eye, ear, face, or neck.
  • ✗When the malformation has been completely corrected surgically.
  • ✗When the condition is a result of trauma or injury.
  • ✗When the condition is due to a disease or disorder developed later in life.

Code Exclusions

Always verify exclusions with the patient's medical history and the physician's documentation.

Documentation Requirements

Accurate documentation is crucial for coding congenital malformations of the eye, ear, face, and neck. The documentation should clearly specify the type of malformation, its location, and any associated conditions or complications.

Clinical Information:

  • •Specific type and location of the malformation.
  • •Any associated conditions or complications.
  • •Laterality, if applicable.
  • •Any surgical corrections or ongoing treatments.
  • •Confirmation that the malformation is congenital.

Supporting Evidence:

  • •Medical history records.
  • •Physical examination findings.
  • •Imaging studies, if applicable.
  • •Surgical reports, if applicable.
Good Documentation Example:

Patient has a congenital malformation of the right ear, specifically anotia, affecting hearing. No surgical correction has been done.

Poor Documentation Example:

Patient has a problem with the right ear.

Common Documentation Errors:

  • âš Not specifying the type of malformation.
  • âš Not documenting the location of the malformation.
  • âš Not confirming that the malformation is congenital.
  • âš Not coding for laterality when applicable.

Range Statistics

9
Total Codes
55
Billable
Complexity:
Medium
Primary Use:Clinical Documentation
Chapter:17

Coding Complexity

Medium
Complexity Rating

Coding for congenital malformations of the eye, ear, face, and neck can be moderately complex due to the need to accurately identify the specific type and location of the malformation, any associated conditions or complications, and the need to confirm that the malformation is congenital.

Key Factors:
  • â–¸Understanding the specific type of malformation.
  • â–¸Determining the correct location of the malformation.
  • â–¸Identifying any associated conditions or complications.
  • â–¸Coding for laterality when applicable.
  • â–¸Confirming that the malformation is congenital.

Specialty Focus

These codes are commonly used in pediatrics, otolaryngology, and ophthalmology. They are crucial for documenting congenital malformations, guiding treatment plans, and tracking patient outcomes.

Primary Specialties:
Pediatrics
40%
Otolaryngology
30%
Ophthalmology
30%
Clinical Scenarios:
  • • A newborn diagnosed with a congenital cleft lip.
  • • A child with a congenital malformation of the ear affecting hearing.
  • • A patient with a congenital malformation of the eye causing vision problems.
  • • A patient with a congenital malformation of the neck causing functional issues.
  • • A patient with a history of congenital facial malformations that have been surgically corrected.

Resources & References

Several resources are available for coding congenital malformations of the eye, ear, face, and neck. These include the official ICD-10 guidelines, coding clinic advice, and various clinical references.

Official Guidelines:

  • ICD-10-CM Official Guidelines for Coding and Reporting
  • AHA Coding Clinic for ICD-10-CM and ICD-10-PCS
  • National Center for Health Statistics (NCHS) ICD-10 guidelines

Clinical References:

  • American Academy of Pediatrics guidelines
  • American Academy of Otolaryngology–Head and Neck Surgery guidelines
  • American Academy of Ophthalmology guidelines

Educational Materials:

  • AAPC ICD-10 training materials
  • AHIMA ICD-10 coding resources
  • CMS ICD-10 coding resources

Frequently Asked Questions

Can I use these codes for acquired deformities?

No, the Q10-Q18 category is specifically for congenital malformations. For acquired deformities, use codes from the M20-M27 range.