Congenital malformations of eye, ear, face and neck
ICD-10 Codes (108)
Q21Q21.0Q21.1Q21.10Q21.11Q21.12Q21.13Q21.14Q21.15Q21.16Q21.19Q21.2Q21.20Q21.21Q21.22Q21.23Q21.3Q21.4Q21.8Q21.9Q22Q22.0Q22.1Q22.2Q22.3Q22.4Q22.5Q22.6Q22.8Q22.9Q23Q23.0Q23.1Q23.2Q23.3Q23.4Q23.8Q23.81Q23.82Q23.88Q23.9Q24Q24.0Q24.1Q24.2Q24.3Q24.4Q24.5Q24.6Q24.8Q24.9Q25Q25.0Q25.1Q25.2Q25.21Q25.29Q25.3Q25.4Q25.40Q25.41Q25.42Q25.43Q25.44Q25.45Q25.46Q25.47Q25.48Q25.49Q25.5Q25.6Q25.7Q25.71Q25.72Q25.79Q25.8Q25.9Q26Q26.0Q26.1Q26.2Q26.3Q26.4Q26.5Q26.6Q26.8Q26.9Q27Q27.0Q27.1Q27.2Q27.3Q27.30Q27.31Q27.32Q27.33Q27.34Q27.39Q27.4Q27.8Q27.9Q28Q28.0Q28.1Q28.2Q28.3Q28.8Q28.9Updates & Changes
FY 2026 Updates
New Codes (1)
Revised Codes (1)
Deleted Codes
No codes deleted in this range for FY 2026
Historical Changes
- •FY 2025: Routine maintenance updates with minor terminology clarifications
- •FY 2024: Enhanced specificity requirements for certain code ranges
- •FY 2023: Updated documentation guidelines for improved clarity
Upcoming Changes
- •Proposed updates pending review by Coordination and Maintenance Committee
- •Under consideration: Enhanced digital health integration codes
Implementation Guidance
- •Review all FY 2026 updates for Q20-Q28 codes before implementation
- •Always verify the most current codes in the ICD-10-CM manual
- •Ensure clinical documentation supports the selected diagnosis codes
- +3 more guidance items...
Range Overview
The ICD-10 category Q20-Q28 encompasses congenital malformations of the eye, ear, face, and neck. These codes are used to document congenital conditions, which are present from birth. This range includes a variety of conditions such as congenital malformations of eyelid, lacrimal apparatus and orbit, congenital malformations of ear causing hearing impairment, cleft lip and cleft palate, and other congenital malformations of face and neck.
Key Usage Points:
- •Always code to the highest level of specificity.
- •Use additional codes to identify any associated conditions.
- •If a patient has multiple congenital malformations, each should be coded separately.
- •For newborns, also use a code from Z38, Liveborn infants, to identify birth status.
- •Remember to code also any associated syndromes.
Coding Guidelines
When to Use:
- ✓When a patient presents with a congenital malformation of the eye, ear, face, or neck.
- ✓When a patient has a history of a congenital malformation that impacts their current health status.
- ✓When a patient's congenital malformation is being surgically corrected.
- ✓When a patient's congenital malformation is causing other health complications.
When NOT to Use:
- ✗When a patient's condition is acquired, not congenital.
- ✗When a patient's condition is not related to the eye, ear, face, or neck.
- ✗When a patient's condition is not a malformation, but a different type of disorder.
- ✗When the condition is not present, but there is a family history of it.
Code Exclusions
Always check the ICD-10 manual for the latest exclusions as they can change with each update.
Documentation Requirements
Proper documentation for congenital malformations of the eye, ear, face, and neck should include specific details about the condition. This includes the exact malformation, its location, any related conditions or complications, and any surgical procedures performed or planned.
Clinical Information:
- •Specific type of malformation
- •Location of the malformation
- •Any related conditions or complications
- •Any surgical procedures performed or planned
- •Impact on patient's health status
Supporting Evidence:
- •Medical history and physical examination findings
- •Imaging studies
- •Surgical reports
- •Consultation notes
Good Documentation Example:
Patient has a congenital malformation of the right ear causing hearing impairment. The malformation is a microtia. No related conditions or complications at this time. Surgical correction is planned.
Poor Documentation Example:
Patient has a malformed ear.
Common Documentation Errors:
- âš Not specifying the exact type of malformation
- âš Not indicating the location of the malformation
- âš Not documenting related conditions or complications
- âš Not documenting surgical procedures
Range Statistics
Coding Complexity
Coding for congenital malformations of the eye, ear, face, and neck can be moderately complex. It requires a detailed understanding of the specific malformations, related conditions, and any surgical procedures. Additionally, guidelines for these codes can change, requiring coders to stay updated.
Key Factors:
- â–¸Understanding the specific type of malformation
- â–¸Identifying any related conditions or complications
- â–¸Coding any surgical procedures
- â–¸Keeping up with changes in coding guidelines
Specialty Focus
These codes are primarily used in pediatrics, otolaryngology (ENT), and ophthalmology. They are also relevant for plastic surgeons who perform corrective surgeries.
Primary Specialties:
Clinical Scenarios:
- • A newborn diagnosed with cleft lip and palate.
- • A child with congenital glaucoma.
- • An adult seeking correction for a congenital ear malformation causing hearing loss.
- • A patient with Goldenhar syndrome, which includes several face and neck malformations.
Resources & References
Several resources are available for coding congenital malformations of the eye, ear, face, and neck. These include the official ICD-10 guidelines, clinical references, and educational materials.
Official Guidelines:
- ICD-10-CM Official Guidelines for Coding and Reporting
- American Health Information Management Association (AHIMA) guidelines
- Centers for Disease Control and Prevention (CDC) guidelines
Clinical References:
- American Academy of Pediatrics guidelines
- American Academy of Ophthalmology guidelines
- American Academy of Otolaryngology–Head and Neck Surgery guidelines
Educational Materials:
- ICD-10-CM Coding Handbook
- Medical Coding Pro ICD-10 resources
- AAPC ICD-10 training materials
Frequently Asked Questions
Can I use these codes for acquired malformations?
No, these codes are specifically for congenital malformations, which are present from birth. Acquired malformations should be coded differently.