Q30-Q38
Medium Complexity

Congenital malformations of the circulatory system

Primary Specialty: Pediatrics
Last Updated: 2025-09-10

ICD-10 Codes (58)

52 billable
0 category headers
Q31
Congenital malformations of larynx
View
Q31.0
Billable
Web of larynx
View
Q31.1
Billable
Congenital subglottic stenosis
View
Q31.2
Billable
Laryngeal hypoplasia
View
Q31.3
Billable
Laryngocele
View
Q31.5
Billable
Congenital laryngomalacia
View
Q31.8
Billable
Other congenital malformations of larynx
View
Q31.9
Billable
Congenital malformation of larynx, unspecified
View
Q32
Billable
Congenital malformations of trachea and bronchus
View
Q32.0
Billable
Congenital tracheomalacia
View
Q32.1
Billable
Other congenital malformations of trachea
View
Q32.2
Billable
Congenital bronchomalacia
View
Q32.3
Billable
Congenital stenosis of bronchus
View
Q32.4
Billable
Other congenital malformations of bronchus
View
Q33
Congenital malformations of lung
View
Q33.0
Billable
Congenital cystic lung
View
Q33.1
Billable
Accessory lobe of lung
View
Q33.2
Billable
Sequestration of lung
View
Q33.3
Billable
Agenesis of lung
View
Q33.4
Billable
Congenital bronchiectasis
View
Q33.5
Billable
Ectopic tissue in lung
View
Q33.6
Billable
Congenital hypoplasia and dysplasia of lung
View
Q33.8
Billable
Other congenital malformations of lung
View
Q33.9
Billable
Congenital malformation of lung, unspecified
View
Q34
Other congenital malformations of respiratory system
View
Q34.0
Billable
Anomaly of pleura
View
Q34.1
Billable
Congenital cyst of mediastinum
View
Q34.8
Billable
Other specified congenital malformations of respiratory system
View
Q34.9
Billable
Congenital malformation of respiratory system, unspecified
View
Q35
Cleft palate
View
Q35.1
Billable
Cleft hard palate
View
Q35.3
Billable
Cleft soft palate
View
Q35.5
Billable
Cleft hard palate with cleft soft palate
View
Q35.7
Billable
Cleft uvula
View
Q35.9
Billable
Cleft palate, unspecified
View
Q36
Billable
Cleft lip
View
Q36.0
Billable
Cleft lip, bilateral
View
Q36.1
Billable
Cleft lip, median
View
Q36.9
Billable
Cleft lip, unilateral
View
Q37
Cleft palate with cleft lip
View
Q37.0
Billable
Cleft hard palate with bilateral cleft lip
View
Q37.1
Billable
Cleft hard palate with unilateral cleft lip
View
Q37.2
Billable
Cleft soft palate with bilateral cleft lip
View
Q37.3
Billable
Cleft soft palate with unilateral cleft lip
View
Q37.4
Billable
Cleft hard and soft palate with bilateral cleft lip
View
Q37.5
Billable
Cleft hard and soft palate with unilateral cleft lip
View
Q37.8
Billable
Unspecified cleft palate with bilateral cleft lip
View
Q37.9
Billable
Unspecified cleft palate with unilateral cleft lip
View
Q38
Other congenital malformations of tongue, mouth and pharynx
View
Q38.0
Billable
Congenital malformations of lips, not elsewhere classified
View
Q38.1
Billable
Ankyloglossia
View
Q38.2
Billable
Macroglossia
View
Q38.3
Billable
Other congenital malformations of tongue
View
Q38.4
Billable
Congenital malformations of salivary glands and ducts
View
Q38.5
Billable
Congenital malformations of palate, not elsewhere classified
View
Q38.6
Billable
Other congenital malformations of mouth
View
Q38.7
Billable
Congenital pharyngeal pouch
View
Q38.8
Billable
Other congenital malformations of pharynx
View

Updates & Changes

FY 2026 Updates

Current Year

New Codes (1)

Q23.4
Hypoplastic left heart syndrome with mitral atresia

Revised Codes (1)

Q21.0
Ventricular septal defect - updated to include hemodynamic significance when known

Deleted Codes

No codes deleted in this range for FY 2026

Historical Changes

  • •FY 2025: Routine maintenance updates with minor terminology clarifications
  • •FY 2024: Enhanced specificity requirements for certain code ranges
  • •FY 2023: Updated documentation guidelines for improved clarity

Upcoming Changes

  • •Proposed updates pending review by Coordination and Maintenance Committee
  • •Under consideration: Enhanced digital health integration codes

Implementation Guidance

  • •Review all FY 2026 updates for Q30-Q38 codes before implementation
  • •Always verify the most current codes in the ICD-10-CM manual
  • •Ensure clinical documentation supports the selected diagnosis codes
  • +3 more guidance items...

Range Overview

high priority

The ICD-10 category Q30-Q38 pertains to congenital malformations of the respiratory system. These codes are used to document congenital anomalies, such as malformations of the nose, larynx, trachea, bronchus, lung, and other parts of the respiratory system. They also cover congenital malformations of the circulatory system, including those of the heart, arteries, veins, and other vessels.

Key Usage Points:

  • •Use these codes for congenital malformations diagnosed at any age, not just in infants or children.
  • •Always code to the highest level of specificity, using additional characters if available.
  • •Use additional codes to identify any associated conditions or complications.
  • •Remember that these codes are not used for acquired conditions or diseases of the respiratory or circulatory systems.
  • •When coding for congenital malformations of the heart, be sure to specify the exact type of malformation.

Coding Guidelines

When to Use:

  • ✓When a patient is diagnosed with a congenital malformation of the respiratory or circulatory system.
  • ✓When a congenital malformation is the cause of a patient's symptoms or condition.
  • ✓When a congenital malformation is discovered during a routine physical examination.
  • ✓When a congenital malformation is found during a diagnostic imaging procedure.

When NOT to Use:

  • ✗When a patient has an acquired disease or condition of the respiratory or circulatory system.
  • ✗When a patient has a temporary or reversible condition of the respiratory or circulatory system.
  • ✗When a patient has a condition that is not related to a congenital malformation.
  • ✗When a patient's condition is due to an injury or trauma.

Code Exclusions

Always verify exclusions with the latest version of the ICD-10-CM Official Guidelines for Coding and Reporting.

Documentation Requirements

Proper documentation for these codes should include a detailed description of the congenital malformation, its location, and any associated conditions or complications. The patient's medical history, physical examination findings, and diagnostic test results should also be documented.

Clinical Information:

  • •Detailed description of the congenital malformation
  • •Location of the malformation
  • •Associated conditions or complications
  • •Patient's medical history
  • •Physical examination findings

Supporting Evidence:

  • •Diagnostic imaging reports
  • •Laboratory test results
  • •Operative reports
  • •Consultation notes
Good Documentation Example:

Patient has a congenital malformation of the heart, specifically a ventricular septal defect. This was confirmed by echocardiogram.

Poor Documentation Example:

Patient has a heart defect.

Common Documentation Errors:

  • âš Not documenting the specific type of congenital malformation
  • âš Not including the location of the malformation
  • âš Not providing supporting evidence from diagnostic tests
  • âš Not documenting associated conditions or complications

Range Statistics

9
Total Codes
52
Billable
Complexity:
Medium
Primary Use:Clinical Documentation
Chapter:17

Coding Complexity

Medium
Complexity Rating

These codes have a medium complexity rating because they require a detailed understanding of the anatomy and physiology of the respiratory and circulatory systems, as well as the ability to distinguish between congenital and acquired conditions. They also require the ability to code to the highest level of specificity and to use additional codes for associated conditions or complications.

Key Factors:
  • â–¸The need to code to the highest level of specificity
  • â–¸The need to use additional codes for associated conditions or complications
  • â–¸The need to distinguish between congenital and acquired conditions
  • â–¸The need to verify exclusions

Specialty Focus

These codes are primarily used by pediatricians, cardiologists, pulmonologists, and other specialists who diagnose and treat congenital malformations of the respiratory and circulatory systems.

Primary Specialties:
Pediatrics
40%
Cardiology
30%
Pulmonology
20%
Clinical Scenarios:
  • • A newborn is diagnosed with a congenital diaphragmatic hernia.
  • • A child is found to have a patent ductus arteriosus during a routine physical examination.
  • • A teenager is diagnosed with a congenital malformation of the nose after complaining of chronic nasal congestion.
  • • An adult is found to have a congenital malformation of the lung during a diagnostic imaging procedure for an unrelated condition.

Resources & References

Resources for these codes include the ICD-10-CM Official Guidelines for Coding and Reporting, the American Academy of Pediatrics, the American Heart Association, and the American Thoracic Society.

Official Guidelines:

  • ICD-10-CM Official Guidelines for Coding and Reporting
  • American Academy of Pediatrics
  • American Heart Association

Clinical References:

  • American Thoracic Society
  • Radiology Society of North America

Educational Materials:

  • AAPC
  • AHIMA

Frequently Asked Questions

Can these codes be used for acquired diseases or conditions of the respiratory or circulatory systems?

No, these codes are only used for congenital malformations. Acquired diseases or conditions should be coded with the appropriate codes from other sections of the ICD-10.