Q50-Q56
Medium Complexity
Congenital malformations of genital organs
Primary Specialty: Obstetrics and Gynecology
Last Updated: 2025-09-10
ICD-10 Codes (102)
96 billable0 category headers
Q51Q51.0Billable
Q51.1Billable
Q51.10Billable
Q51.11Billable
Q51.2Billable
Q51.21Billable
Q51.22Billable
Q51.28Billable
Q51.3Billable
Q51.4Billable
Q51.5Billable
Q51.6Billable
Q51.7Billable
Q51.8Billable
Q51.81Billable
Q51.810Billable
Q51.811Billable
Q51.818Billable
Q51.82Billable
Q51.820Billable
Q51.821Billable
Q51.828Billable
Q51.9Billable
Q52Q52.0Billable
Q52.1Billable
Q52.10Billable
Q52.11Billable
Q52.12Billable
Q52.120Billable
Q52.121Billable
Q52.122Billable
Q52.123Billable
Q52.124Billable
Q52.129Billable
Q52.2Billable
Q52.3Billable
Q52.4Billable
Q52.5Billable
Q52.6Billable
Q52.7Billable
Q52.70Billable
Q52.71Billable
Q52.79Billable
Q52.8Billable
Q52.9Billable
Q53Q53.0Billable
Q53.00Billable
Q53.01Billable
Q53.02Billable
Q53.1Billable
Q53.10Billable
Q53.11Billable
Q53.111Billable
Q53.112Billable
Q53.12Billable
Q53.13Billable
Q53.2Billable
Q53.20Billable
Q53.21Billable
Q53.211Billable
Q53.212Billable
Q53.22Billable
Q53.23Billable
Q53.9Billable
Q54Q54.0Billable
Q54.1Billable
Q54.2Billable
Q54.3Billable
Q54.4Billable
Q54.8Billable
Q54.9Billable
Q55Q55.0Billable
Q55.1Billable
Q55.2Billable
Q55.20Billable
Q55.21Billable
Q55.22Billable
Q55.23Billable
Q55.29Billable
Q55.3Billable
Q55.4Billable
Q55.5Billable
Q55.6Billable
Q55.61Billable
Q55.62Billable
Q55.63Billable
Q55.64Billable
Q55.69Billable
Q55.7Billable
Q55.8Billable
Q55.9Billable
Q56Q56.0Billable
Q56.1Billable
Q56.2Billable
Q56.3Billable
Q56.4Billable
Updates & Changes
FY 2026 Updates
Current Year
New Codes (1)
Q23.4
Hypoplastic left heart syndrome with mitral atresia
Revised Codes (1)
Q21.0
Ventricular septal defect - updated to include hemodynamic significance when known
Deleted Codes
No codes deleted in this range for FY 2026
Historical Changes
- •FY 2025: Routine maintenance updates with minor terminology clarifications
- •FY 2024: Enhanced specificity requirements for certain code ranges
- •FY 2023: Updated documentation guidelines for improved clarity
Upcoming Changes
- •Proposed updates pending review by Coordination and Maintenance Committee
- •Under consideration: Enhanced digital health integration codes
Implementation Guidance
- •Review all FY 2026 updates for Q50-Q56 codes before implementation
- •Always verify the most current codes in the ICD-10-CM manual
- •Ensure clinical documentation supports the selected diagnosis codes
- +3 more guidance items...
Range Overview
high priority
The ICD-10 code range Q50-Q56 represents congenital malformations of genital organs. These codes are used to document various types of congenital abnormalities, both male and female, that are present at birth. The range includes specific codes for conditions such as undescended testicle (Q53), congenital absence of uterus and cervix (Q51), and other malformations of the genital organs. These codes are crucial for accurate medical documentation and statistical tracking of these congenital conditions.
Key Usage Points:
- •Always use specific codes that identify the exact type of congenital malformation.
- •When coding for undescended testicle, specify the side (left, right, bilateral).
- •For conditions like congenital absence of uterus, use additional codes to identify any associated endocrine disorder.
- •In case of multiple malformations, each should be coded separately.
- •When coding for intersex disorders, use additional codes to specify any associated sexual dysfunction.
Coding Guidelines
When to Use:
- ✓When a patient presents with a congenital malformation of the genital organs.
- ✓If a patient has a history of a congenital genital malformation that impacts their current health status.
- ✓When a patient undergoes surgery for correction of a congenital genital malformation.
- ✓If a patient has a congenital genital malformation and an associated endocrine disorder.
- ✓When a patient presents with an intersex disorder due to a congenital malformation.
When NOT to Use:
- ✗When a patient has an acquired malformation of the genital organs.
- ✗If the patient's condition is due to a disease or injury, not a congenital malformation.
- ✗When the patient's congenital malformation has been corrected and no longer impacts their health.
- ✗If the patient has a genital malformation, but it is not congenital.
- ✗When the patient's condition is not specified as congenital.
Code Exclusions
Always verify exclusions with the latest version of the ICD-10 coding manual.
Documentation Requirements
Proper documentation for congenital malformations of genital organs should clearly specify the type of malformation, its location, and any associated conditions. It should also include information on how the condition impacts the patient's health and any treatment provided.
Clinical Information:
- •Specific type of congenital malformation
- •Location of the malformation
- •Associated conditions or complications
- •Impact on patient's health
- •Treatment provided or planned
Supporting Evidence:
- •Medical history
- •Physical examination findings
- •Imaging studies
- •Surgical reports
Good Documentation Example:
Patient with congenital absence of uterus and associated endocrine disorder. Condition impacts fertility. Hormone replacement therapy planned.
Poor Documentation Example:
Patient with genital malformation.
Common Documentation Errors:
- âš Not specifying the type of malformation
- âš Failing to code for associated conditions
- âš Not indicating how the condition impacts the patient's health
- âš Not documenting treatment provided or planned
Range Statistics
7
Total Codes
96
Billable
Complexity:
Medium
Primary Use:Clinical Documentation
Chapter:17
Coding Complexity
Medium
Complexity Rating
Coding for congenital malformations of genital organs is of medium complexity due to the need to accurately identify the specific type of malformation and any associated conditions. It also requires an understanding of how the condition impacts the patient's health and keeping up-to-date with changes in coding guidelines.
Key Factors:
- â–¸Identifying the specific type of malformation
- â–¸Coding for associated conditions
- â–¸Understanding the impact on patient's health
- â–¸Keeping up-to-date with changes in coding guidelines
Specialty Focus
These codes are most commonly used in specialties dealing with reproductive health and endocrinology. They are also relevant in pediatric care, especially in cases of intersex disorders.
Primary Specialties:
Obstetrics and Gynecology
40%
Urology
30%
Pediatrics
20%
Endocrinology
10%
Clinical Scenarios:
- • A newborn diagnosed with undescended testicle
- • A woman with congenital absence of uterus seeking fertility treatment
- • A child with an intersex disorder due to a congenital malformation
- • A patient undergoing surgery for correction of a congenital genital malformation
- • A patient with a history of congenital genital malformation that impacts their current health status
Resources & References
Numerous resources are available for coders working with ICD-10 codes for congenital malformations of genital organs. These include the official ICD-10 coding manual, clinical reference materials, and educational resources.
Official Guidelines:
- ICD-10-CM Official Guidelines for Coding and Reporting
- World Health Organization's ICD-10 online version
- National Center for Health Statistics ICD-10-CM webpage
- American Health Information Management Association's ICD-10 resources
Clinical References:
- UpToDate
- Medscape
- PubMed
Educational Materials:
- American Academy of Professional Coders' ICD-10 training
- American Health Information Management Association's ICD-10 training
- Medical Coding Academy's ICD-10 courses
Frequently Asked Questions
Can I use a code from this range for an acquired malformation of the genital organs?
No, the codes in this range are specifically for congenital malformations. Acquired malformations should be coded elsewhere.