Q60-Q64
Medium Complexity

Congenital malformations of the urinary system

Primary Specialty: Urology
Last Updated: 2025-09-10

ICD-10 Codes (68)

64 billable
0 category headers
Q61
Cystic kidney disease
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Q61.0
Billable
Congenital renal cyst
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Q61.00
Billable
Congenital renal cyst, unspecified
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Q61.01
Billable
Congenital single renal cyst
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Q61.02
Billable
Congenital multiple renal cysts
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Q61.1
Billable
Polycystic kidney, infantile type
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Q61.11
Billable
Cystic dilatation of collecting ducts
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Q61.19
Billable
Other polycystic kidney, infantile type
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Q61.2
Billable
Polycystic kidney, adult type
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Q61.3
Billable
Polycystic kidney, unspecified
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Q61.4
Billable
Renal dysplasia
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Q61.5
Billable
Medullary cystic kidney
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Q61.8
Billable
Other cystic kidney diseases
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Q61.9
Billable
Cystic kidney disease, unspecified
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Q62
Congenital obstructive defects of renal pelvis and congenital malformations of ureter
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Q62.0
Billable
Congenital hydronephrosis
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Q62.1
Billable
Congenital occlusion of ureter
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Q62.10
Billable
Congenital occlusion of ureter, unspecified
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Q62.11
Billable
Congenital occlusion of ureteropelvic junction
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Q62.12
Billable
Congenital occlusion of ureterovesical orifice
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Q62.2
Billable
Congenital megaureter
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Q62.3
Billable
Other obstructive defects of renal pelvis and ureter
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Q62.31
Billable
Congenital ureterocele, orthotopic
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Q62.32
Billable
Cecoureterocele
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Q62.39
Billable
Other obstructive defects of renal pelvis and ureter
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Q62.4
Billable
Agenesis of ureter
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Q62.5
Billable
Duplication of ureter
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Q62.6
Billable
Malposition of ureter
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Q62.60
Billable
Malposition of ureter, unspecified
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Q62.61
Billable
Deviation of ureter
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Q62.62
Billable
Displacement of ureter
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Q62.63
Billable
Anomalous implantation of ureter
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Q62.69
Billable
Other malposition of ureter
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Q62.7
Billable
Congenital vesico-uretero-renal reflux
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Q62.8
Billable
Other congenital malformations of ureter
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Q63
Other congenital malformations of kidney
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Q63.0
Billable
Accessory kidney
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Q63.1
Billable
Lobulated, fused and horseshoe kidney
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Q63.2
Billable
Ectopic kidney
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Q63.3
Billable
Hyperplastic and giant kidney
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Q63.8
Billable
Other specified congenital malformations of kidney
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Q63.9
Billable
Congenital malformation of kidney, unspecified
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Q64
Other congenital malformations of urinary system
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Q64.0
Billable
Epispadias
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Q64.1
Billable
Exstrophy of urinary bladder
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Q64.10
Billable
Exstrophy of urinary bladder, unspecified
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Q64.11
Billable
Supravesical fissure of urinary bladder
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Q64.12
Billable
Cloacal exstrophy of urinary bladder
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Q64.19
Billable
Other exstrophy of urinary bladder
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Q64.2
Billable
Congenital posterior urethral valves
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Q64.3
Billable
Other atresia and stenosis of urethra and bladder neck
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Q64.31
Billable
Congenital bladder neck obstruction
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Q64.32
Billable
Congenital stricture of urethra
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Q64.33
Billable
Congenital stricture of urinary meatus
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Q64.39
Billable
Other atresia and stenosis of urethra and bladder neck
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Q64.4
Billable
Malformation of urachus
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Q64.5
Billable
Congenital absence of bladder and urethra
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Q64.6
Billable
Congenital diverticulum of bladder
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Q64.7
Billable
Other and unspecified congenital malformations of bladder and urethra
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Q64.70
Billable
Unspecified congenital malformation of bladder and urethra
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Q64.71
Billable
Congenital prolapse of urethra
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Q64.72
Billable
Congenital prolapse of urinary meatus
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Q64.73
Billable
Congenital urethrorectal fistula
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Q64.74
Billable
Double urethra
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Q64.75
Billable
Double urinary meatus
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Q64.79
Billable
Other congenital malformations of bladder and urethra
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Q64.8
Billable
Other specified congenital malformations of urinary system
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Q64.9
Billable
Congenital malformation of urinary system, unspecified
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Updates & Changes

FY 2026 Updates

Current Year

New Codes (1)

Q23.4
Hypoplastic left heart syndrome with mitral atresia

Revised Codes (1)

Q21.0
Ventricular septal defect - updated to include hemodynamic significance when known

Deleted Codes

No codes deleted in this range for FY 2026

Historical Changes

  • •FY 2025: Routine maintenance updates with minor terminology clarifications
  • •FY 2024: Enhanced specificity requirements for certain code ranges
  • •FY 2023: Updated documentation guidelines for improved clarity

Upcoming Changes

  • •Proposed updates pending review by Coordination and Maintenance Committee
  • •Under consideration: Enhanced digital health integration codes

Implementation Guidance

  • •Review all FY 2026 updates for Q60-Q64 codes before implementation
  • •Always verify the most current codes in the ICD-10-CM manual
  • •Ensure clinical documentation supports the selected diagnosis codes
  • +3 more guidance items...

Range Overview

high priority

The ICD-10 code range Q60-Q64 pertains to congenital malformations of the urinary system. These codes are used to document conditions such as renal agenesis and dysgenesis, cystic kidney disease, and other congenital anomalies of kidney and urinary tract. The codes provide a detailed classification system for these congenital conditions, allowing for precise documentation and tracking of patient health data.

Key Usage Points:

  • •Always code to the highest level of specificity within the Q60-Q64 range.
  • •Use additional codes to identify any associated conditions or complications.
  • •Remember to code for laterality when applicable.
  • •Use combination codes for conditions that have both a specified type and a specified site.
  • •Always verify the code in the Tabular List before finalizing.

Coding Guidelines

When to Use:

  • ✓When a patient is diagnosed with a congenital malformation of the urinary system.
  • ✓When a patient's congenital urinary system condition is a factor in their current health status or treatment.
  • ✓When a patient has a history of a congenital urinary system condition that affects their current health.
  • ✓When a patient has a complication or secondary condition resulting from a congenital urinary system malformation.

When NOT to Use:

  • ✗When the condition is acquired, not congenital.
  • ✗When the condition is not confirmed by the provider.
  • ✗When the condition is not relevant to the current episode of care.
  • ✗When the condition has been previously coded and has no bearing on the current episode of care.

Code Exclusions

Always verify exclusions in the Tabular List to ensure accurate coding.

Documentation Requirements

Proper documentation for codes within the Q60-Q64 range requires detailed clinical information, including the specific type and location of the malformation, any associated conditions or complications, and the impact of the condition on the patient's health status. Documentation should be clear, concise, and specific.

Clinical Information:

  • •Specific type of malformation
  • •Location of malformation
  • •Laterality, if applicable
  • •Associated conditions or complications
  • •Impact on patient's health status

Supporting Evidence:

  • •Diagnostic test results
  • •Imaging studies
  • •Operative reports
  • •Clinical notes
Good Documentation Example:

Patient diagnosed with bilateral renal agenesis, confirmed by ultrasound. Condition impacting kidney function and overall health status.

Poor Documentation Example:

Patient has kidney issue.

Common Documentation Errors:

  • âš Not specifying the type of malformation
  • âš Not coding for laterality
  • âš Not including associated conditions or complications
  • âš Not verifying the code in the Tabular List

Range Statistics

5
Total Codes
64
Billable
Complexity:
Medium
Primary Use:Clinical Documentation
Chapter:17

Coding Complexity

Medium
Complexity Rating

The coding complexity for the Q60-Q64 range is rated as medium due to the need for a high level of specificity, the use of combination codes, and the need to code for laterality. Additionally, coders must be aware of associated conditions or complications and understand the exclusions within this range.

Key Factors:
  • â–¸Need for high level of specificity
  • â–¸Use of combination codes
  • â–¸Coding for laterality
  • â–¸Associated conditions or complications
  • â–¸Exclusion of certain conditions

Specialty Focus

The Q60-Q64 codes are primarily used in specialties such as urology, nephrology, and pediatrics. These codes are crucial for tracking patient outcomes, conducting research, and planning resources in these fields.

Primary Specialties:
Urology
40%
Nephrology
30%
Pediatrics
30%
Clinical Scenarios:
  • • A newborn diagnosed with polycystic kidney disease.
  • • A child with a congenital bladder anomaly requiring surgical intervention.
  • • A patient with a history of renal dysgenesis presenting with kidney failure.
  • • A patient with a congenital ureter anomaly causing recurrent urinary tract infections.

Resources & References

Numerous resources are available for coding within the Q60-Q64 range, including the official ICD-10 guidelines, clinical reference materials, and educational resources.

Official Guidelines:

  • ICD-10-CM Official Guidelines for Coding and Reporting
  • American Health Information Management Association (AHIMA) guidelines
  • American Hospital Association (AHA) Coding Clinic

Clinical References:

  • Urology textbooks
  • Nephrology journals
  • Pediatric medicine resources

Educational Materials:

  • ICD-10 coding courses
  • Webinars on congenital urinary system malformations
  • Coding practice exercises

Frequently Asked Questions

Can I use a Q60-Q64 code for an acquired condition of the urinary system?

No, the Q60-Q64 range is specifically for congenital malformations. Acquired conditions should be coded elsewhere in the ICD-10.