Cutaneous mastocytosis
ICD-10 D47.01 is a billable code used to indicate a diagnosis of cutaneous mastocytosis.
Cutaneous mastocytosis is a rare skin disorder characterized by an abnormal accumulation of mast cells in the skin. This condition typically presents in infancy or early childhood, manifesting as reddish-brown macules, papules, or plaques that may be itchy or have a tendency to urticate upon pressure or friction, a phenomenon known as Darier's sign. The mast cells in cutaneous mastocytosis can release histamine and other mediators, leading to symptoms such as flushing, pruritus, and in some cases, anaphylaxis. While cutaneous mastocytosis is generally considered benign, there is a potential for progression to systemic mastocytosis, particularly in cases that persist into adulthood. Surveillance is crucial, as patients may develop systemic symptoms or complications over time. Diagnosis is typically confirmed through skin biopsy, which reveals an increased number of mast cells. Treatment focuses on symptom management, including antihistamines for pruritus and avoidance of triggers that may provoke mast cell degranulation. Regular follow-up is recommended to monitor for any signs of progression to systemic involvement.
Detailed descriptions of skin lesions, biopsy results, and patient history.
Diagnosis of cutaneous mastocytosis in pediatric patients, management of pruritus, and monitoring for systemic symptoms.
Ensure accurate documentation of the clinical presentation and any associated symptoms to support the diagnosis.
Records of allergic reactions, patient history of mast cell-related symptoms, and treatment responses.
Management of mast cell activation symptoms, evaluation of potential triggers, and treatment with antihistamines.
Document any systemic symptoms that may indicate progression to systemic mastocytosis.
Used when a biopsy is performed to confirm the diagnosis of cutaneous mastocytosis.
Document the reason for the biopsy, the site, and the findings.
Dermatologists should ensure that the biopsy results are clearly linked to the diagnosis.
Common symptoms include reddish-brown macules or papules, itching, and the presence of Darier's sign, where lesions urticate upon pressure.
Diagnosis is typically made through clinical evaluation and confirmed with a skin biopsy showing an increased number of mast cells.
While cutaneous mastocytosis is generally benign, there is a risk of progression to systemic mastocytosis, which can be more serious.
Treatment focuses on symptom management, including antihistamines for itching and avoiding known triggers.
