Hb-SS disease with crisis
ICD-10 D57.0 is a billable code used to indicate a diagnosis of hb-ss disease with crisis.
Hb-SS disease, commonly known as sickle cell disease, is a genetic blood disorder characterized by the presence of hemoglobin S (HbS) in red blood cells. This condition leads to the distortion of red blood cells into a sickle shape, particularly under low oxygen conditions. Patients with Hb-SS disease experience recurrent painful episodes known as sickle cell crises, which occur due to vaso-occlusion caused by the sickled cells obstructing blood flow in small vessels. These crises can lead to acute pain, organ damage, and increased risk of infections. The disease is inherited in an autosomal recessive pattern, meaning that both parents must carry the sickle cell trait for a child to be affected. Management of Hb-SS disease includes pain management, hydration, blood transfusions, and hydroxyurea therapy to reduce the frequency of crises. Regular monitoring and preventive care are essential to manage complications such as acute chest syndrome, stroke, and organ dysfunction.
Detailed clinical notes on patient history, frequency of crises, and treatment plans.
Management of acute pain crises, blood transfusion therapy, and monitoring for complications.
Ensure accurate documentation of laboratory results, including hemoglobin electrophoresis.
Growth and development assessments, vaccination status, and family history of sickle cell disease.
Routine check-ups, management of pain crises, and preventive care.
Documenting parental education on disease management and crisis prevention.
Used during acute crises requiring blood transfusion.
Document the reason for transfusion, type of blood product, and patient response.
Hematology specialists should ensure compliance with transfusion protocols.
Hb-SS disease is a severe form of sickle cell disease characterized by significant health complications, while sickle cell trait is a carrier state that typically does not cause symptoms or health issues.
