Hb-SS disease with crisis, unspecified
ICD-10 D57.00 is a billable code used to indicate a diagnosis of hb-ss disease with crisis, unspecified.
Hb-SS disease, commonly known as sickle cell disease, is a genetic blood disorder characterized by the production of abnormal hemoglobin, known as hemoglobin S (HbS). This condition leads to the distortion of red blood cells into a sickle or crescent shape, which can cause blockages in blood vessels, leading to pain crises and other complications. Patients with Hb-SS disease often experience episodes of severe pain, known as sickle cell crises, due to vaso-occlusive events. These crises can be triggered by various factors, including dehydration, infection, and extreme temperatures. The disease is inherited in an autosomal recessive pattern, meaning that both parents must carry the sickle cell trait for a child to be affected. The clinical management of Hb-SS disease includes pain management, hydration, and preventive measures against infections. Regular monitoring and comprehensive care are essential to manage complications such as acute chest syndrome, stroke, and organ damage. The unspecified crisis designation indicates that the specific type of crisis (e.g., vaso-occlusive, acute chest syndrome) has not been documented, which may affect treatment and management strategies.
Detailed patient history, including family history of sickle cell disease, frequency and type of crises, and treatment plans.
Management of pain crises, acute chest syndrome, and chronic complications of sickle cell disease.
Ensure accurate documentation of crisis type and associated complications to support coding.
Growth and development assessments, vaccination history, and management of complications in pediatric patients.
Routine check-ups, management of pain episodes, and preventive care.
Consider age-specific guidelines and the impact of sickle cell disease on development.
Used for routine blood tests in patients with sickle cell disease.
Document the reason for blood collection and any relevant patient history.
Ensure that the procedure is linked to the diagnosis of Hb-SS disease.
Hb-SS disease is a severe form of sickle cell disease characterized by the presence of two copies of the sickle cell gene, leading to significant health complications. In contrast, sickle cell trait occurs when an individual has one copy of the sickle cell gene and one normal gene, typically resulting in no symptoms or complications.
