Hb-SS disease with crisis with other specified complication
ICD-10 D57.09 is a billable code used to indicate a diagnosis of hb-ss disease with crisis with other specified complication.
Hb-SS disease, also known as sickle cell disease, is a genetic blood disorder characterized by the presence of hemoglobin S (HbS). This condition leads to the distortion of red blood cells into a sickle shape, which can cause blockages in blood vessels, leading to pain crises and other complications. Patients with Hb-SS disease often experience hemolytic anemia due to the rapid breakdown of sickle-shaped cells, leading to a variety of symptoms including fatigue, jaundice, and increased risk of infections. The 'crisis' refers to episodes of severe pain, often in the chest, abdomen, or joints, caused by vaso-occlusive events. The 'other specified complication' may include acute chest syndrome, stroke, or organ damage, which can arise from the disease's progression or from specific triggers such as dehydration or infection. Management of Hb-SS disease requires a multidisciplinary approach, including pain management, hydration, and possibly blood transfusions or hydroxyurea therapy to reduce the frequency of crises and complications.
Detailed clinical notes on patient history, crisis episodes, and treatment plans.
Management of pain crises, blood transfusions, and complications like acute chest syndrome.
Ensure documentation reflects the severity and frequency of crises for accurate coding.
Growth and development assessments, vaccination status, and family history of sickle cell disease.
Routine management of sickle cell disease in children, including preventive care and crisis management.
Documenting the impact of the disease on the child's daily activities and school performance.
Used during hospitalization for severe anemia due to sickle cell disease.
Document the indication for transfusion and patient response.
Hematology specialists should ensure that the transfusion protocol is followed.
Hb-SS disease is a severe form of sickle cell disease characterized by significant health complications, while sickle cell trait is a carrier state that typically does not cause symptoms or complications.
