Sickle-cell/Hb-C disease with crisis
ICD-10 D57.21 is a billable code used to indicate a diagnosis of sickle-cell/hb-c disease with crisis.
Sickle-cell/Hb-C disease with crisis refers to a specific type of hemolytic anemia characterized by the presence of both sickle hemoglobin (HbS) and hemoglobin C (HbC). This condition arises from genetic mutations affecting the beta-globin gene, leading to the production of abnormal hemoglobin. Patients with this disease experience recurrent painful crises due to vaso-occlusive events, where sickle-shaped red blood cells obstruct blood flow in small vessels. This can result in acute pain episodes, organ damage, and increased risk of infections. The crisis can be triggered by various factors, including dehydration, infection, and extreme temperatures. Management typically involves pain control, hydration, and sometimes blood transfusions. Understanding the genetic basis of this condition is crucial, as it is inherited in an autosomal recessive pattern, meaning that both parents must carry the gene for a child to be affected. Regular monitoring and preventive care are essential to manage complications and improve quality of life for affected individuals.
Detailed patient history, genetic testing results, and documentation of crisis episodes.
Management of pain crises, blood transfusions, and monitoring for complications.
Ensure accurate documentation of the type of hemoglobinopathy and associated symptoms.
Growth and development assessments, family history of hemoglobinopathies, and vaccination status.
Routine check-ups, management of acute crises, and preventive care.
Consider age-related factors in symptom presentation and management.
Used during management of severe anemia or crisis.
Document the reason for transfusion and patient response.
Hematology specialists should ensure compliance with transfusion protocols.
D57.21 indicates sickle-cell/Hb-C disease with crisis, while D57.22 refers to the same disease without crisis. Accurate documentation of crisis episodes is essential for correct coding.
