Sickle-cell/Hb-C disease with cerebral vascular involvement
ICD-10 D57.213 is a billable code used to indicate a diagnosis of sickle-cell/hb-c disease with cerebral vascular involvement.
Sickle-cell/Hb-C disease with cerebral vascular involvement is a complex hemolytic anemia characterized by the presence of both sickle hemoglobin (HbS) and hemoglobin C (HbC). This condition arises from genetic mutations in the HBB gene, leading to abnormal hemoglobin production. Patients with this disease often experience vaso-occlusive crises, hemolytic anemia, and increased risk of stroke due to cerebral vascular involvement. The sickling of red blood cells can obstruct blood flow in small vessels, resulting in ischemia and potential neurological deficits. Clinical manifestations may include recurrent pain episodes, fatigue, and complications such as acute chest syndrome and stroke. Management typically involves pain control, hydration, and preventive measures against infections and stroke. Regular monitoring and comprehensive care are essential to mitigate complications and improve quality of life.
Detailed patient history, lab results showing hemoglobin types, and evidence of complications.
Management of pain crises, monitoring for stroke, and treatment of infections.
Ensure documentation reflects the severity of anemia and any neurological assessments.
Neurological evaluations, imaging studies (e.g., MRI), and detailed descriptions of symptoms.
Evaluation of stroke symptoms in patients with sickle cell disease.
Document the relationship between sickle cell disease and neurological findings.
Used for routine blood tests to monitor hemoglobin levels.
Document the reason for blood draw and any relevant clinical findings.
Hematology specialists should ensure comprehensive lab results are included.
Coding D57.213 accurately reflects the complexity of sickle-cell/Hb-C disease with cerebral vascular involvement, ensuring appropriate management and reimbursement for the care provided.
