Sickle-cell thalassemia, unspecified, with splenic sequestration
ICD-10 D57.412 is a billable code used to indicate a diagnosis of sickle-cell thalassemia, unspecified, with splenic sequestration.
Sickle-cell thalassemia is a genetic blood disorder characterized by the presence of both sickle cell disease and thalassemia, leading to abnormal hemoglobin production. In this condition, the red blood cells can become rigid and sickle-shaped, which can obstruct blood flow and lead to various complications, including splenic sequestration. Splenic sequestration occurs when sickled red blood cells accumulate in the spleen, causing it to enlarge and potentially leading to a sudden drop in hemoglobin levels. This can result in severe anemia and requires immediate medical attention. Patients may experience symptoms such as abdominal pain, fatigue, and pallor. The management of sickle-cell thalassemia with splenic sequestration often involves blood transfusions, hydration, and pain management, along with monitoring for further complications. Genetic counseling is also essential for affected individuals and their families to understand the inheritance patterns and risks associated with this condition.
Detailed clinical notes on hemoglobin levels, splenic size, and treatment responses.
Management of acute splenic sequestration crises, chronic anemia management, and transfusion protocols.
Ensure accurate documentation of genetic testing and family history.
Family history, genetic testing results, and counseling notes.
Genetic counseling for families with a history of sickle cell disease or thalassemia.
Documentation of inheritance patterns and potential risks for offspring.
Used during acute splenic sequestration management.
Document the indication for transfusion and patient response.
Hematology specialists should ensure compliance with transfusion protocols.
Splenic sequestration is a critical complication that can lead to severe anemia and requires prompt medical intervention. It is essential to document this condition accurately to ensure appropriate management and coding.
