Sickle-cell thalassemia beta plus with crisis with other specified complication
ICD-10 D57.458 is a billable code used to indicate a diagnosis of sickle-cell thalassemia beta plus with crisis with other specified complication.
Sickle-cell thalassemia beta plus is a complex hemoglobinopathy resulting from the combination of sickle cell disease and beta-thalassemia. Patients with this condition exhibit symptoms of both disorders, including chronic hemolytic anemia, vaso-occlusive crises, and potential complications such as infections and organ damage. The 'with crisis' designation indicates the presence of acute episodes characterized by severe pain due to vaso-occlusion, which can lead to further complications. The 'with other specified complication' aspect highlights that the patient may experience additional issues, such as acute chest syndrome, splenic sequestration, or stroke, which require careful monitoring and management. Genetic factors play a significant role in the pathophysiology of this condition, as it is inherited in an autosomal recessive manner. Understanding the interplay between sickle cell and thalassemia is crucial for effective treatment and management, as it influences the severity of symptoms and the risk of complications.
Comprehensive documentation of patient history, genetic testing results, and detailed descriptions of crises and complications.
Management of acute pain crises, monitoring for acute chest syndrome, and treatment of infections.
Ensure accurate coding of complications and crises to reflect the severity of the patient's condition.
Documentation of family history, genetic testing results, and counseling notes.
Genetic counseling for families, interpretation of genetic tests, and management of hereditary conditions.
Highlight the importance of genetic factors in the patient's condition for accurate coding.
Used for routine blood tests to monitor hemoglobin levels and complications.
Document the reason for blood draw and any relevant clinical findings.
Ensure that the specialty performing the procedure is noted.
The 'with crisis' designation indicates that the patient is experiencing acute episodes of pain or other complications related to sickle-cell thalassemia beta plus, which requires immediate medical attention and management.
