Other sickle-cell disorders with acute chest syndrome
ICD-10 D57.811 is a billable code used to indicate a diagnosis of other sickle-cell disorders with acute chest syndrome.
D57.811 refers to a specific condition within the spectrum of sickle cell disorders characterized by the presence of acute chest syndrome (ACS). ACS is a severe complication of sickle cell disease, presenting with chest pain, fever, cough, and respiratory distress. It is primarily caused by vaso-occlusive crises leading to pulmonary infarction, infection, or fat embolism. Patients with sickle cell disorders experience hemolytic anemia due to the destruction of sickle-shaped red blood cells, which can lead to various complications, including acute chest syndrome. Genetic factors play a crucial role in the severity and frequency of these episodes, with different mutations in the HBB gene affecting hemoglobin structure and function. Management of ACS often requires hospitalization, oxygen therapy, pain management, and sometimes blood transfusions to alleviate symptoms and prevent further complications. Understanding the nuances of this condition is essential for accurate coding and appropriate patient management.
Detailed patient history, lab results, and treatment plans must be documented.
Management of acute chest syndrome in patients with sickle cell disease.
Genetic testing results and family history may be relevant for comprehensive care.
Documentation of respiratory assessments, imaging results, and treatment responses.
Evaluation and management of respiratory distress in patients with ACS.
Coordination with hematology for comprehensive management of sickle cell complications.
Used during hospitalization for severe anemia due to acute chest syndrome.
Document the need for transfusion based on hemoglobin levels and clinical symptoms.
Hematology should be involved in the decision-making process for transfusions.
Coding D57.811 accurately reflects the presence of acute chest syndrome in patients with sickle cell disorders, which is critical for appropriate treatment and management.