Von Willebrand disease, type 2N
ICD-10 D68.023 is a billable code used to indicate a diagnosis of von willebrand disease, type 2n.
Von Willebrand disease (VWD) is a hereditary bleeding disorder caused by a deficiency or dysfunction of von Willebrand factor (VWF), a protein essential for platelet adhesion and aggregation. Type 2N is characterized by a qualitative defect in VWF that leads to a reduced ability of VWF to bind to factor VIII, resulting in a bleeding tendency similar to that seen in hemophilia A. Patients with type 2N may present with symptoms such as easy bruising, prolonged bleeding from cuts, heavy menstrual bleeding, and spontaneous bleeding episodes. Diagnosis is typically confirmed through laboratory tests that assess VWF levels and function, as well as factor VIII levels. Management may include desmopressin (DDAVP) to increase VWF levels, and in severe cases, factor VIII concentrates may be necessary. Understanding the nuances of this condition is crucial for accurate coding and appropriate patient management.
Comprehensive documentation of bleeding history, laboratory results, and treatment plans.
Patients presenting with unexplained bleeding, family history of bleeding disorders, or requiring surgical intervention.
Ensure that all laboratory tests are clearly documented, including VWF antigen and activity levels.
Detailed patient history and physical examination findings related to bleeding symptoms.
Routine check-ups for patients with known bleeding disorders or referrals to specialists.
Document any referrals to hematology for further evaluation and management.
Used to evaluate overall blood health and detect anemia or thrombocytopenia.
Document the reason for the CBC and any relevant findings.
Hematology specialists may require additional tests to assess bleeding disorders.
Type 2N is primarily caused by a qualitative defect in von Willebrand factor that affects its ability to bind factor VIII, leading to a bleeding tendency.
