Von Willebrand disease, type 3
ICD-10 D68.03 is a billable code used to indicate a diagnosis of von willebrand disease, type 3.
Von Willebrand disease (VWD) type 3 is a rare, inherited bleeding disorder characterized by a severe deficiency or absence of von Willebrand factor (VWF), a protein crucial for platelet adhesion and aggregation. This condition leads to significant coagulation defects, resulting in prolonged bleeding episodes, easy bruising, and excessive bleeding from minor injuries or surgical procedures. Patients may experience spontaneous bleeding, particularly from mucosal surfaces such as the nose and gums, and may also have heavy menstrual bleeding (menorrhagia). The severity of bleeding in type 3 VWD is often comparable to that seen in severe hemophilia. Diagnosis typically involves laboratory tests to measure VWF levels and activity, as well as factor VIII levels, which are often low in these patients. Management may include desmopressin administration, VWF concentrates, and supportive care during bleeding episodes. Due to the complexity of the disorder and its management, accurate coding is essential for appropriate treatment and reimbursement.
Detailed lab results, family history, and treatment plans.
Management of bleeding episodes, pre-operative assessments.
Ensure documentation reflects the severity and frequency of bleeding episodes.
Genetic testing results and family pedigree.
Counseling for family members, genetic testing for at-risk individuals.
Documenting inheritance patterns and implications for family planning.
Used for laboratory testing to confirm VWD diagnosis.
Document the reason for blood draw and any relevant clinical history.
Ensure that the specialty performing the blood draw is noted.
The primary treatment for Von Willebrand disease type 3 includes the administration of von Willebrand factor concentrates and desmopressin to manage bleeding episodes and prevent excessive bleeding during surgical procedures.
