Evans syndrome
ICD-10 D69.41 is a billable code used to indicate a diagnosis of evans syndrome.
Evans syndrome is a rare autoimmune disorder characterized by the simultaneous occurrence of autoimmune hemolytic anemia (AIHA) and immune thrombocytopenic purpura (ITP). Patients with Evans syndrome typically present with symptoms of anemia, such as fatigue, pallor, and shortness of breath, alongside signs of thrombocytopenia, including easy bruising, petechiae, and increased bleeding tendencies. The pathophysiology involves the production of autoantibodies that target red blood cells and platelets, leading to their destruction in the spleen and other parts of the reticuloendothelial system. Diagnosis is often confirmed through laboratory tests showing low hemoglobin levels, low platelet counts, and the presence of specific autoantibodies. Treatment may include corticosteroids, immunosuppressive agents, and in some cases, splenectomy. Due to the overlapping nature of the symptoms and the need for careful management of both anemia and thrombocytopenia, Evans syndrome poses unique challenges in clinical practice and coding.
Detailed lab results, treatment plans, and follow-up notes are essential.
Patients presenting with unexplained anemia and thrombocytopenia.
Ensure clear documentation of both hemolytic anemia and thrombocytopenia to support coding.
Documentation of autoimmune markers and response to immunosuppressive therapy.
Patients with recurrent infections and autoimmune symptoms.
Document the autoimmune nature of the condition and any associated disorders.
Used to evaluate anemia and thrombocytopenia in patients suspected of having Evans syndrome.
Ensure lab results are documented in the patient's record.
Hematology specialists should document the rationale for ordering CBC and any follow-up tests.
Evans syndrome is an autoimmune disorder characterized by the simultaneous presence of autoimmune hemolytic anemia and immune thrombocytopenic purpura, leading to low red blood cell and platelet counts.
