IgG4-related disease
ICD-10 D89.84 is a billable code used to indicate a diagnosis of igg4-related disease.
IgG4-related disease is a systemic condition characterized by elevated serum IgG4 levels and the infiltration of IgG4-positive plasma cells in various tissues. This condition can affect multiple organs, including the pancreas, salivary glands, kidneys, and lymph nodes, leading to a range of symptoms such as swelling, pain, and dysfunction of the affected organs. The disease is often misdiagnosed due to its diverse presentations, which can mimic other conditions such as autoimmune diseases and malignancies. Diagnosis typically involves imaging studies, serological tests for IgG4 levels, and histopathological examination of biopsies. Treatment usually includes corticosteroids, which can lead to significant improvement in symptoms and organ function. However, the management of IgG4-related disease can be complex due to the potential for relapse and the need for long-term monitoring.
Detailed clinical notes on symptoms, lab results, and treatment plans.
Patients presenting with unexplained organ dysfunction, elevated IgG4 levels, or symptoms mimicking other autoimmune diseases.
Ensure comprehensive documentation of all affected organs and treatment responses to support the diagnosis.
Endoscopic findings, imaging results, and biopsy reports for gastrointestinal involvement.
Patients with pancreatic masses or autoimmune pancreatitis.
Document the correlation between imaging findings and laboratory results to substantiate the diagnosis.
Used to confirm elevated IgG4 levels in suspected cases.
Document the reason for testing and the results.
Rheumatologists and immunologists should ensure comprehensive lab documentation.
Common symptoms include swelling of affected organs, pain, jaundice, and unexplained weight loss. Symptoms can vary widely depending on the organs involved.
