Carcinoid heart syndrome
ICD-10 E34.01 is a billable code used to indicate a diagnosis of carcinoid heart syndrome.
Carcinoid heart syndrome is a condition that arises in patients with carcinoid tumors, which are neuroendocrine tumors that primarily secrete serotonin and other vasoactive substances. This syndrome is characterized by the development of fibrous plaques on the right side of the heart, leading to valvular heart disease, particularly affecting the tricuspid and pulmonary valves. The syndrome typically occurs in patients with metastatic carcinoid tumors, especially those originating in the gastrointestinal tract or pancreas. Symptoms may include heart murmurs, right-sided heart failure, and signs of systemic venous congestion. The pathophysiology involves the release of serotonin and other substances into the systemic circulation, which can lead to fibrosis of the heart valves and endocardium. Diagnosis is often confirmed through echocardiography, which reveals characteristic valvular abnormalities. Management may involve treating the underlying carcinoid tumor, symptomatic relief, and in some cases, surgical intervention for valvular repair or replacement.
Detailed echocardiographic findings and clinical correlation with carcinoid syndrome.
Patients presenting with right-sided heart failure symptoms and known carcinoid tumors.
Ensure clear documentation of valvular involvement and any surgical interventions.
Comprehensive tumor staging and treatment history.
Patients undergoing treatment for carcinoid tumors with cardiac symptoms.
Document the relationship between tumor burden and cardiac manifestations.
Used to assess cardiac function in patients with carcinoid heart syndrome.
Echocardiographic findings must be documented.
Cardiology specialists should ensure comprehensive reporting of findings.
Common symptoms include shortness of breath, fatigue, palpitations, and signs of right-sided heart failure such as edema and ascites.
