Eisenmenger's syndrome
ICD-10 I27.83 is a billable code used to indicate a diagnosis of eisenmenger's syndrome.
Eisenmenger's syndrome is a complex condition characterized by the development of pulmonary arterial hypertension (PAH) due to a long-standing left-to-right shunt, typically resulting from congenital heart defects such as ventricular septal defect (VSD) or atrial septal defect (ASD). Over time, the increased blood flow to the lungs leads to vascular remodeling and elevated pulmonary artery pressures, eventually causing a reversal of the shunt to a right-to-left direction. Clinically, patients may present with symptoms such as cyanosis, exertional dyspnea, fatigue, and signs of right heart failure. The anatomy involved includes the heart's chambers, particularly the right ventricle, and the pulmonary arteries. Disease progression can lead to severe complications, including arrhythmias, thromboembolic events, and decreased exercise tolerance. Diagnostic considerations include echocardiography, cardiac catheterization, and pulmonary function tests to assess the severity of PAH and the underlying structural heart defects. Early recognition and management are crucial to improving outcomes and quality of life for affected individuals.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
I27.83 specifically covers Eisenmenger's syndrome, which arises from congenital heart defects leading to pulmonary arterial hypertension. It is characterized by a right-to-left shunt due to elevated pulmonary pressures.
I27.83 should be used when the patient has established Eisenmenger's syndrome with a documented right-to-left shunt due to pulmonary hypertension, differentiating it from other types of pulmonary hypertension.
Documentation should include echocardiographic findings, evidence of pulmonary hypertension, details of congenital heart defects, and clinical symptoms consistent with Eisenmenger's syndrome.
