Obstructive hypertrophic cardiomyopathy
ICD-10 I42.1 is a billable code used to indicate a diagnosis of obstructive hypertrophic cardiomyopathy.
Obstructive hypertrophic cardiomyopathy (HCM) is a genetic cardiovascular disorder characterized by abnormal thickening of the heart muscle, particularly affecting the interventricular septum. This hypertrophy can obstruct blood flow from the left ventricle to the aorta, leading to symptoms such as dyspnea, chest pain, palpitations, and syncope. The condition often presents in adolescents or young adults but can occur at any age. The anatomy involved includes the left ventricle, interventricular septum, and mitral valve apparatus, which may also be affected by the hypertrophy. Disease progression can lead to heart failure, arrhythmias, and sudden cardiac death, particularly in younger patients. Diagnosis typically involves echocardiography, which reveals the characteristic thickening of the heart muscle, and may be supplemented by MRI or genetic testing to confirm the diagnosis and assess family history. Clinical management may include lifestyle modifications, medications such as beta-blockers, and in severe cases, surgical interventions like septal myectomy or alcohol septal ablation.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
I42.1 specifically covers obstructive hypertrophic cardiomyopathy, characterized by significant left ventricular hypertrophy that obstructs outflow. It is often associated with symptoms of heart failure and arrhythmias.
I42.1 should be used when there is documented obstructive hypertrophic cardiomyopathy, as opposed to I42.0, which is for hypertrophic cardiomyopathy without obstruction. The distinction is crucial for treatment and management.
Documentation should include a detailed clinical history, results from echocardiograms showing left ventricular hypertrophy, and any relevant genetic testing results. Clear evidence of obstruction during cardiac imaging is also necessary.
