Endocardial fibroelastosis
ICD-10 I42.4 is a billable code used to indicate a diagnosis of endocardial fibroelastosis.
Endocardial fibroelastosis (EFE) is a rare cardiac condition characterized by the thickening of the endocardium, primarily affecting the left ventricle. This condition is often seen in infants and young children, particularly those with congenital heart defects. Clinically, patients may present with symptoms of heart failure, including dyspnea, fatigue, and poor growth. The anatomy involved includes the endocardial layer of the heart, which becomes fibrotic and elastotic, leading to impaired cardiac function. Disease progression can vary, but untreated EFE can lead to severe heart failure and arrhythmias. Diagnosis typically involves echocardiography, which reveals thickened endocardial layers and may show associated ventricular dilation. MRI and cardiac catheterization may also be utilized for further assessment. Early diagnosis and intervention are crucial to improve outcomes, as the condition can lead to significant morbidity and mortality if not managed appropriately.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
I42.4 specifically covers endocardial fibroelastosis, which is characterized by the thickening of the endocardium. It is often associated with congenital heart defects and can lead to heart failure.
I42.4 should be used when a patient has a confirmed diagnosis of endocardial fibroelastosis, particularly when imaging studies demonstrate the characteristic endocardial thickening, distinguishing it from other forms of cardiomyopathy.
Documentation should include clinical findings, echocardiographic evidence of endocardial thickening, and any relevant history of congenital heart disease. Detailed notes on symptoms and treatment plans are also necessary.
