Idiopathic interstitial pneumonia, not otherwise specified
ICD-10 J84.111 is a billable code used to indicate a diagnosis of idiopathic interstitial pneumonia, not otherwise specified.
Idiopathic interstitial pneumonia (IIP) is a group of lung diseases characterized by inflammation and scarring (fibrosis) of the lung tissue. The term 'idiopathic' indicates that the cause of the condition is unknown. Clinically, patients may present with progressive dyspnea (shortness of breath), a persistent dry cough, and fatigue. Physical examination may reveal crackles on auscultation and signs of respiratory distress. The disease primarily affects the interstitial lung tissue, which is the area surrounding the air sacs (alveoli) in the lungs. Over time, the inflammation can lead to irreversible lung damage and respiratory failure. Diagnostic considerations include high-resolution computed tomography (HRCT) scans, which can reveal characteristic patterns of lung involvement, and lung biopsy, which may be necessary to confirm the diagnosis. Pulmonary function tests often show restrictive lung disease patterns. Early diagnosis and management are crucial to slowing disease progression and improving quality of life.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
J84.111 specifically covers idiopathic interstitial pneumonia, which includes various forms of IIP such as idiopathic pulmonary fibrosis (IPF) when no other underlying cause is identified. It is essential to differentiate it from secondary interstitial lung diseases caused by known factors like autoimmune diseases or environmental exposures.
J84.111 should be used when a patient presents with idiopathic interstitial pneumonia that cannot be attributed to any known cause. If there is evidence of a specific underlying condition, other codes should be considered, such as J84.10 for unspecified interstitial lung disease.
Documentation supporting J84.111 should include a thorough clinical evaluation, imaging studies (preferably HRCT), pulmonary function tests, and any relevant laboratory results. A detailed history that rules out other potential causes of interstitial lung disease is also critical.
