Idiopathic pulmonary fibrosis
ICD-10 J84.112 is a billable code used to indicate a diagnosis of idiopathic pulmonary fibrosis.
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive lung disease characterized by the accumulation of scar tissue (fibrosis) in the lungs, leading to a decline in lung function. The etiology of IPF remains unknown, hence the term 'idiopathic.' Clinically, patients typically present with symptoms such as persistent dry cough, dyspnea (shortness of breath), and fatigue. The disease primarily affects the interstitial lung tissue, which is crucial for gas exchange. As the fibrosis progresses, the lungs become increasingly stiff, making it difficult for patients to breathe and leading to respiratory failure. Diagnostic considerations include high-resolution computed tomography (HRCT) scans, which reveal characteristic patterns of lung fibrosis, and pulmonary function tests that demonstrate restrictive lung disease. A multidisciplinary approach is often required for diagnosis, including ruling out other interstitial lung diseases and conducting a thorough clinical evaluation. Early diagnosis and management are crucial as IPF has a poor prognosis, with a median survival of 3-5 years post-diagnosis.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
J84.112 specifically covers idiopathic pulmonary fibrosis, which is characterized by progressive lung scarring without a known cause. It is distinct from other interstitial lung diseases that may have identifiable causes.
J84.112 should be used when the diagnosis of idiopathic pulmonary fibrosis is confirmed, particularly when other causes of interstitial lung disease have been ruled out through clinical evaluation and imaging.
Documentation should include a comprehensive clinical history, results from high-resolution CT scans showing typical patterns of fibrosis, pulmonary function test results indicating restrictive lung disease, and any relevant laboratory tests to exclude other conditions.
