Cicatricial pemphigoid
ICD-10 L12.1 is a billable code used to indicate a diagnosis of cicatricial pemphigoid.
Cicatricial pemphigoid, also known as benign mucous membrane pemphigoid, is an autoimmune blistering disorder primarily affecting the mucous membranes, particularly the oral cavity, conjunctiva, and occasionally the skin. Clinically, it presents with painful blisters that can lead to scarring and adhesions, especially in the eyes, which may result in vision impairment. The disease is characterized by the presence of autoantibodies against components of the basement membrane zone, leading to subepithelial blister formation. The progression of cicatricial pemphigoid can be chronic, with periods of exacerbation and remission. Diagnosis is typically confirmed through a combination of clinical examination, histopathological analysis, and direct immunofluorescence studies showing linear deposition of IgG and complement at the basement membrane. Early diagnosis and management are crucial to prevent complications such as scarring and functional impairment of affected mucosal sites.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
L12.1 specifically covers cicatricial pemphigoid, which primarily affects mucous membranes and can lead to scarring. It is distinct from other forms of pemphigoid, such as bullous pemphigoid, which primarily affects the skin.
L12.1 should be used when the clinical presentation aligns with cicatricial pemphigoid, particularly when there is evidence of mucosal involvement and scarring. It is important to differentiate it from other blistering disorders based on clinical findings and diagnostic tests.
Documentation should include clinical findings of blistering lesions, histopathological confirmation, results from immunofluorescence studies, and treatment plans. Detailed notes on the patient's history and response to treatment are also essential.
