Café au lait spots
ICD-10 L81.3 is a billable code used to indicate a diagnosis of café au lait spots.
Café au lait spots are flat, pigmented lesions that vary in size and are typically light brown in color, resembling the color of coffee with milk. These skin manifestations are often present at birth or develop in early childhood. They are caused by an increase in melanin production in the skin and are most commonly found on the trunk, buttocks, and extremities. While café au lait spots are benign and do not pose any health risks, their presence can be associated with certain genetic conditions, such as neurofibromatosis type 1 (NF1). The diagnosis is primarily clinical, based on the appearance and distribution of the spots, and may require genetic counseling if multiple lesions are present. Disease progression is generally stable, but the number and size of spots can increase with age. Diagnostic considerations include a thorough patient history and physical examination to rule out associated syndromes. In cases where café au lait spots are numerous, further evaluation for underlying conditions may be warranted.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
L81.3 specifically covers café au lait spots, which are benign pigmented lesions. It is important to note that while the spots themselves are not harmful, their presence can indicate a higher risk for neurofibromatosis type 1 and other genetic conditions.
L81.3 should be used when documenting café au lait spots specifically. If the lesions are part of a broader condition or if they are atypical in appearance, other codes may be more appropriate.
Documentation should include a detailed description of the café au lait spots, including their size, number, and location. Family history and any associated symptoms should also be documented to support the diagnosis and rule out related conditions.
