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ICD-10 Guide
ICD-10 CodesN07.4

N07.4

Billable

Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/18/2025

Code Description

ICD-10 N07.4 is a billable code used to indicate a diagnosis of hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis.

Key Diagnostic Point:

N07.4 refers to a specific type of hereditary nephropathy characterized by diffuse endocapillary proliferative glomerulonephritis. This condition is often associated with genetic mutations that affect kidney function, leading to proteinuria and potential progression to chronic kidney disease. Patients may present with isolated proteinuria, which is a key indicator of glomerular dysfunction. The hereditary nature of this nephropathy suggests a genetic predisposition, often requiring genetic testing for accurate diagnosis and management. The diffuse endocapillary proliferative pattern indicates an inflammatory response within the glomeruli, which can be identified through renal biopsy. This condition is not classified under other specific nephropathies, making accurate coding essential for proper treatment and management.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Requires understanding of hereditary nephropathies and their genetic basis.
  • Involves distinguishing between various types of glomerulonephritis.
  • Documentation must clearly indicate the hereditary nature and specific glomerular involvement.
  • Potential for overlapping symptoms with other renal conditions.

Audit Risk Factors

  • Inadequate documentation of hereditary factors.
  • Failure to specify the type of glomerulonephritis.
  • Misclassification with other nephropathies.
  • Lack of genetic testing results in the medical record.

Specialty Focus

Medical Specialties

Nephrology

Documentation Requirements

Detailed renal function tests, biopsy results, and genetic testing outcomes.

Common Clinical Scenarios

Patients presenting with unexplained proteinuria, family history of kidney disease, or abnormal renal function tests.

Billing Considerations

Ensure that genetic testing results are included in the documentation to support the hereditary diagnosis.

Genetics

Documentation Requirements

Genetic test results, family history documentation, and clinical findings related to hereditary nephropathy.

Common Clinical Scenarios

Patients with a known family history of kidney disease undergoing genetic evaluation.

Billing Considerations

Documentation should clearly link genetic findings to clinical symptoms and nephropathy diagnosis.

Coding Guidelines

Inclusion Criteria

Use N07.4 When
  • According to ICD
  • 10 coding guidelines, N07
  • 4 should be used when the condition is specifically documented as hereditary nephropathy with diffuse endocapillary proliferative glomerulonephritis
  • It is important to ensure that the documentation supports the hereditary nature and the specific glomerular involvement

Exclusion Criteria

Do NOT use N07.4 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

88305CPT Code

Pathology examination of renal biopsy

Clinical Scenario

Used when a renal biopsy is performed to confirm the diagnosis of nephropathy.

Documentation Requirements

Pathology report must be included in the medical record.

Specialty Considerations

Nephrologists should ensure that biopsy findings correlate with clinical symptoms.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of hereditary nephropathies, improving the accuracy of diagnoses and treatment plans. N07.4 provides a clear classification for hereditary nephropathy with specific glomerular involvement.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of hereditary nephropathies, improving the accuracy of diagnoses and treatment plans. N07.4 provides a clear classification for hereditary nephropathy with specific glomerular involvement.

Reimbursement & Billing Impact

reimbursement and to avoid claim denials.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What is the significance of genetic testing in N07.4?

Genetic testing is crucial for confirming the hereditary nature of the nephropathy and guiding treatment options. It helps in understanding the prognosis and potential familial implications.