Bicuspid aortic valve
ICD-10 Q23.81 is a billable code used to indicate a diagnosis of bicuspid aortic valve.
Bicuspid aortic valve (BAV) is a congenital heart defect characterized by the presence of only two cusps in the aortic valve instead of the normal three. This malformation can lead to various complications, including aortic stenosis, regurgitation, and an increased risk of aortic aneurysm and dissection. BAV is often asymptomatic in childhood but may present with symptoms such as chest pain, shortness of breath, or syncope in later years. The condition is frequently associated with other congenital heart defects, such as coarctation of the aorta and ventricular septal defects. Diagnosis is typically made through echocardiography, which can visualize the valve structure and assess its function. Management may include regular monitoring, medical management of symptoms, and surgical intervention if significant stenosis or regurgitation develops. Understanding the implications of BAV is crucial for pediatric patients, as early detection and intervention can significantly improve long-term outcomes.
Pediatric documentation should include detailed descriptions of the patient's symptoms, echocardiographic findings, and any associated congenital anomalies. Growth and development assessments are also important.
Common scenarios include routine follow-up visits for asymptomatic patients, evaluation of symptoms like exertional dyspnea, and preoperative assessments for surgical intervention.
Coders should be aware of the age-related presentation of symptoms and the need for long-term follow-up in pediatric patients with BAV.
Genetic documentation should include family history, any genetic syndromes associated with BAV, and results from genetic testing if applicable.
Scenarios may include genetic counseling for families with a history of congenital heart defects and evaluation for syndromic associations.
Consideration should be given to the potential genetic basis of BAV and its association with other congenital anomalies.
Used for initial diagnosis and follow-up of BAV.
Documentation must include indications for the echocardiogram and findings related to BAV.
Pediatric cardiologists should ensure that echocardiographic findings are clearly documented.
Patients with BAV are at risk for aortic stenosis, regurgitation, and aortic aneurysm. Regular monitoring and timely intervention are crucial to manage these risks effectively.
