Cor triatriatum
ICD-10 Q24.2 is a billable code used to indicate a diagnosis of cor triatriatum.
Cor triatriatum is a rare congenital heart defect characterized by the presence of a fibrous membrane that divides the left atrium into two chambers, creating a triatrial configuration. This condition can lead to obstruction of blood flow from the pulmonary veins to the left ventricle, resulting in pulmonary hypertension and heart failure if not diagnosed and treated early. Patients may present with symptoms such as difficulty breathing, cyanosis, and exercise intolerance. Diagnosis is typically made through echocardiography, which reveals the abnormal atrial structure and any associated defects. Surgical intervention is often required to remove the obstructive membrane and restore normal blood flow. The prognosis for patients with cor triatriatum varies depending on the presence of other congenital heart defects and the timing of surgical intervention. Early detection and management are crucial for improving outcomes in affected individuals.
Pediatric documentation must include growth parameters, developmental milestones, and specific symptoms related to cardiac function.
Common scenarios include infants presenting with respiratory distress or failure to thrive due to undiagnosed cor triatriatum.
Coders should be aware of the age-related variations in presentation and the importance of early intervention in pediatric patients.
Genetic documentation should include family history of congenital heart defects and any chromosomal abnormalities that may be associated.
Genetic counseling may be required for families with a history of congenital heart defects, including cor triatriatum.
Consideration of syndromic associations is crucial, as cor triatriatum may occur in conjunction with genetic syndromes.
Used during surgical intervention for cor triatriatum to restore normal atrial anatomy.
Operative report detailing the surgical approach and findings.
Pediatric cardiology specialists should provide detailed operative notes.
Common symptoms include difficulty breathing, cyanosis, fatigue, and exercise intolerance. Symptoms may vary based on the severity of the obstruction and the presence of associated congenital defects.
