Interruption of aortic arch
ICD-10 Q25.21 is a billable code used to indicate a diagnosis of interruption of aortic arch.
Interruption of the aortic arch is a rare congenital heart defect characterized by a discontinuity in the aortic arch, which can lead to significant hemodynamic instability. This condition typically presents in neonates and is often associated with other congenital anomalies, including coarctation of the aorta, ventricular septal defects, and other forms of congenital heart disease. The interruption can occur at various locations along the arch, most commonly between the left common carotid artery and the left subclavian artery. Clinical manifestations may include severe hypertension in the upper body and hypotension in the lower body, leading to differential cyanosis. Diagnosis is typically made through echocardiography, MRI, or chest X-ray, which may reveal indirect signs such as a
Detailed clinical notes including physical examination findings, imaging results, and surgical reports are essential for accurate coding.
Neonates presenting with shock or differential cyanosis, requiring urgent echocardiographic evaluation.
Consideration of growth and development post-surgery, as well as the need for long-term follow-up for potential complications.
Genetic testing results, family history of congenital heart defects, and any syndromic associations must be documented.
Cases where interruption of aortic arch is part of a genetic syndrome, such as Turner syndrome or 22q11.2 deletion syndrome.
Awareness of the genetic implications and counseling needs for families with a history of congenital heart defects.
Used during surgical intervention for interruption of the aortic arch.
Operative report detailing the procedure and any associated anomalies.
Pediatric cardiology and cardiothoracic surgery documentation must be thorough.
Common associated conditions include coarctation of the aorta, ventricular septal defects, and syndromic associations such as Turner syndrome and 22q11.2 deletion syndrome. Accurate documentation of these associations is crucial for coding.
