Congenital aneurysm of aorta
ICD-10 Q25.43 is a billable code used to indicate a diagnosis of congenital aneurysm of aorta.
Congenital aneurysm of the aorta is a rare vascular malformation characterized by an abnormal dilation of the aorta that is present at birth. This condition can occur in isolation or in conjunction with other congenital heart defects, such as coarctation of the aorta, ventricular septal defects, or tetralogy of Fallot. The aneurysm may affect any segment of the aorta, including the ascending aorta, aortic arch, or descending aorta. Clinical manifestations can vary widely, ranging from asymptomatic cases discovered incidentally to severe complications such as aortic rupture or dissection, which can be life-threatening. Diagnosis typically involves imaging studies such as echocardiography, MRI, or CT scans. Management may include surgical intervention, particularly in symptomatic patients or those with significant aneurysm size. Long-term follow-up is essential due to the risk of associated cardiovascular complications and the potential for progressive aortic dilation.
Pediatric documentation should include detailed clinical history, physical examination findings, and results from imaging studies. Growth and developmental assessments are also important.
Common scenarios include a newborn presenting with a heart murmur, a child with failure to thrive due to cardiac issues, or a teenager with a known congenital heart defect undergoing routine evaluation.
Coders must ensure that all congenital conditions are documented, including any associated anomalies, to accurately reflect the patient's clinical picture.
Genetic documentation should include family history, genetic testing results, and any syndromic associations with congenital heart defects.
Scenarios may involve genetic counseling for families with a history of congenital heart defects or syndromes associated with aortic aneurysms.
Consideration must be given to the potential genetic syndromes that may predispose patients to congenital aneurysms, such as Marfan syndrome or Turner syndrome.
Used when surgical intervention is performed for a congenital aneurysm.
Operative reports detailing the procedure and indications for surgery.
Pediatric cardiology and surgery must collaborate for accurate coding.
Accurate coding of congenital aneurysms is crucial for appropriate patient management, resource allocation, and understanding the epidemiology of congenital heart defects. It also impacts reimbursement and quality of care metrics.
