Double aortic arch
ICD-10 Q25.45 is a billable code used to indicate a diagnosis of double aortic arch.
Double aortic arch is a congenital vascular anomaly characterized by the presence of two aortic arches that encircle the trachea and esophagus, leading to potential compression of these structures. This condition arises from abnormal development of the embryonic aortic arches during fetal life. Patients may present with respiratory distress, difficulty swallowing, or stridor due to the compression of the trachea and esophagus. Diagnosis is typically confirmed through imaging studies such as echocardiography, MRI, or CT angiography. Surgical intervention is often required to relieve symptoms and prevent complications, making early detection and management crucial. The condition can occur in isolation or in conjunction with other congenital heart defects, such as ventricular septal defects or coarctation of the aorta, necessitating a comprehensive evaluation of the cardiovascular system.
Pediatric documentation should include detailed descriptions of symptoms, imaging results, and any associated congenital anomalies. Growth and developmental assessments are also important.
Common scenarios include infants presenting with respiratory distress or feeding difficulties, requiring urgent evaluation and management.
Consideration of age-specific symptoms and the impact of congenital heart defects on overall health and development is essential.
Genetic documentation should include family history, potential syndromic associations, and results from genetic testing if applicable.
Scenarios may involve genetic counseling for families with a history of congenital heart defects or syndromes associated with double aortic arch.
Awareness of genetic syndromes that may present with double aortic arch is crucial for accurate coding and management.
Used during surgical intervention for double aortic arch.
Document the surgical approach, any complications, and postoperative care.
Pediatric surgical documentation must include details on the patient's age and weight.
Common symptoms include respiratory distress, stridor, difficulty swallowing, and failure to thrive in infants. These symptoms arise due to compression of the trachea and esophagus by the aortic arches.
