Atresia of pulmonary artery
ICD-10 Q25.5 is a billable code used to indicate a diagnosis of atresia of pulmonary artery.
Atresia of the pulmonary artery is a congenital malformation characterized by the complete obstruction of the pulmonary artery, which impedes blood flow from the right ventricle to the lungs. This condition can lead to significant hypoxemia and requires immediate medical intervention. The atresia may occur in isolation or as part of complex congenital heart defects, such as tetralogy of Fallot or pulmonary atresia with ventricular septal defect. Clinical presentation often includes cyanosis, difficulty breathing, and failure to thrive in infants. Diagnosis is typically confirmed through echocardiography, which visualizes the heart's structure and blood flow. Surgical intervention is often necessary to create a pathway for blood flow to the lungs, and long-term follow-up is essential to monitor for complications such as pulmonary hypertension or heart failure. The management of atresia of the pulmonary artery requires a multidisciplinary approach, involving pediatric cardiologists, cardiothoracic surgeons, and geneticists, especially in cases associated with chromosomal abnormalities.
Detailed clinical notes on the infant's growth, development, and response to treatment are essential. Documentation should include echocardiogram results and any surgical interventions performed.
Common scenarios include newborns presenting with cyanosis, requiring immediate evaluation for congenital heart disease, and infants undergoing surgical repair of pulmonary atresia.
Pediatric coders must be aware of the nuances in coding congenital heart defects and the importance of capturing all relevant clinical details.
Genetic testing results and family history should be documented, especially if there is a suspicion of syndromic associations with chromosomal abnormalities.
Scenarios include genetic counseling for families with a history of congenital heart defects and evaluation for syndromes associated with pulmonary atresia.
Genetic coders should ensure accurate coding of any identified chromosomal abnormalities that may be associated with the congenital condition.
Used during surgical intervention for atresia of the pulmonary artery.
Surgical notes detailing the procedure and any complications.
Pediatric cardiothoracic surgeons must ensure accurate coding of the procedure.
Atresia of the pulmonary artery is often associated with other congenital heart defects, such as ventricular septal defects, tetralogy of Fallot, and other structural anomalies. Genetic syndromes may also be present, necessitating thorough evaluation and documentation.
