Total anomalous pulmonary venous connection
ICD-10 Q26.2 is a billable code used to indicate a diagnosis of total anomalous pulmonary venous connection.
Total anomalous pulmonary venous connection (TAPVC) is a congenital heart defect characterized by the abnormal drainage of all four pulmonary veins into the right atrium instead of the left atrium. This condition leads to a lack of oxygenated blood entering the systemic circulation, resulting in cyanosis and respiratory distress in affected infants. TAPVC can be classified into four types: supracardiac, cardiac, infracardiac, and mixed, based on the anatomical location of the anomalous veins. Clinical presentation typically includes tachypnea, retractions, and a heart murmur. Diagnosis is confirmed through echocardiography, which visualizes the abnormal venous connections. Surgical intervention is often required to correct the defect, and early diagnosis is crucial for improving outcomes. The condition is often associated with other congenital heart defects, such as atrial septal defects or ventricular septal defects, necessitating comprehensive evaluation and management.
Detailed clinical notes on symptoms, diagnostic imaging results, and treatment plans.
Infants presenting with respiratory distress and cyanosis, requiring urgent evaluation.
Consideration of age and weight for surgical risk assessment and management.
Family history of congenital heart defects and genetic counseling notes.
Assessment of genetic syndromes associated with congenital heart defects.
Evaluation for chromosomal abnormalities that may accompany TAPVC.
Used during surgical intervention for TAPVC correction.
Operative report detailing the procedure and any complications.
Pediatric cardiology and cardiothoracic surgery documentation standards.
Coding the specific type of TAPVC is crucial for accurate treatment planning, surgical intervention, and understanding the prognosis, as each type may have different implications for management and outcomes.
