Agenesis of lung
ICD-10 Q33.3 is a billable code used to indicate a diagnosis of agenesis of lung.
Agenesis of the lung is a rare congenital malformation characterized by the complete absence of one or both lungs. This condition can occur as an isolated anomaly or as part of a syndrome involving other congenital defects. The absence of lung tissue leads to significant respiratory compromise, often necessitating immediate medical intervention. Agenesis can be unilateral (affecting one lung) or bilateral (affecting both lungs), with unilateral cases generally having a better prognosis. Associated anomalies may include congenital heart defects, tracheoesophageal fistula, and other malformations of the respiratory system. Diagnosis is typically made through imaging studies such as chest X-rays or CT scans, which reveal the absence of lung tissue. Management strategies may involve supportive care, surgical interventions, and addressing any associated congenital anomalies. Early diagnosis and intervention are crucial for improving outcomes in affected infants.
Detailed clinical notes on respiratory status, imaging results, and any interventions performed.
Infants presenting with respiratory distress, requiring evaluation for congenital lung anomalies.
Consideration of the infant's gestational age and overall health status when coding.
Genetic testing results, family history of congenital anomalies, and any syndromic associations.
Cases where lung agenesis is part of a genetic syndrome, requiring genetic counseling.
Documentation of chromosomal abnormalities that may be associated with lung agenesis.
Used in cases of lung resection due to congenital anomalies.
Operative reports detailing the procedure and indications.
Pediatric surgical documentation must include details on congenital conditions.
Lung agenesis refers to the complete absence of lung tissue, while lung hypoplasia indicates underdevelopment of lung tissue. Accurate coding requires distinguishing between these two conditions based on clinical and imaging findings.
