Congenital hypoplasia and dysplasia of lung
ICD-10 Q33.6 is a billable code used to indicate a diagnosis of congenital hypoplasia and dysplasia of lung.
Congenital hypoplasia and dysplasia of the lung refers to underdevelopment (hypoplasia) or abnormal development (dysplasia) of lung tissue that occurs during fetal development. This condition can lead to significant respiratory distress in neonates, as the lungs may not be capable of supporting adequate gas exchange. Hypoplasia can occur due to various factors, including genetic syndromes, environmental exposures, or associated congenital anomalies such as congenital diaphragmatic hernia or oligohydramnios. Dysplastic lung tissue may exhibit abnormal architecture, which can further compromise respiratory function. Clinically, affected infants may present with symptoms such as tachypnea, cyanosis, and retractions shortly after birth. Diagnosis is typically confirmed through imaging studies such as chest X-rays or CT scans, which reveal the extent of lung development. Management may involve supportive care, including oxygen therapy and mechanical ventilation, and in some cases, surgical intervention may be necessary to address associated anomalies.
Documentation should include detailed clinical findings, imaging results, and any interventions performed. It is essential to note the infant's gestational age and any associated congenital conditions.
Common scenarios include infants presenting with respiratory distress due to congenital lung anomalies, requiring NICU admission for management.
Consideration must be given to the infant's overall clinical picture, including any other congenital anomalies that may impact respiratory function.
Genetic evaluations should document any identified chromosomal abnormalities or syndromic associations that may contribute to lung hypoplasia.
Scenarios may include genetic counseling for families with a history of congenital anomalies or syndromes associated with lung hypoplasia.
Genetic testing results should be clearly documented to support the diagnosis and coding of associated conditions.
Used for infants with respiratory distress due to congenital lung hypoplasia.
Document the need for CPAP therapy and the infant's response.
Pediatric specialists should ensure accurate coding for respiratory support.
Documentation should include clinical findings, imaging results, associated congenital anomalies, and any interventions performed. Clear linkage between the diagnosis and treatment is essential for accurate coding.
