ICD-10 Logo
ICDxICD-10 Medical Coding
ICD-10 Logo
ICDxICD-10 Medical Coding
ICD 10 CodesDiagnoses
ICD 10 CodesDiagnoses
ICD-10 Logo
ICDxICD-10 Medical Coding

Comprehensive ICD-10-CM code reference with AI-powered search capabilities.

© 2025 ICD Code Compass. All rights reserved.

Browse

  • All Chapters
  • All Categories
  • Diagnoses

Tools

  • AI Code Search
ICD-10-CM codes are maintained by the CDC and CMS. This tool is for reference purposes only.
v1.0.0
ICD-10 Guide
ICD-10 CodesQ33.8

Q33.8

Billable

Other congenital malformations of lung

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q33.8 is a billable code used to indicate a diagnosis of other congenital malformations of lung.

Key Diagnostic Point:

Congenital malformations of the lung encompass a variety of structural abnormalities that can significantly impact respiratory function. These malformations may include conditions such as lung hypoplasia, where the lung is underdeveloped, leading to inadequate respiratory capacity. Choanal atresia, a condition where the nasal passage is blocked, can also affect breathing, particularly in newborns. Tracheoesophageal fistula, an abnormal connection between the trachea and esophagus, can complicate feeding and breathing. These conditions often require multidisciplinary management, including surgical intervention and ongoing respiratory support. Accurate coding is essential for proper treatment planning and reimbursement, as these congenital conditions can lead to significant morbidity and require specialized care.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and severity of conditions
  • Need for detailed documentation of associated anomalies
  • Potential for multiple congenital conditions in a single patient
  • Differentiation from acquired lung conditions

Audit Risk Factors

  • Inadequate documentation of the specific congenital malformation
  • Failure to capture associated anomalies
  • Incorrect coding of severity or type of malformation
  • Misunderstanding of the relationship between respiratory and feeding issues

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Pediatric documentation must include detailed descriptions of the malformation, associated symptoms, and any interventions performed.

Common Clinical Scenarios

Common scenarios include newborns presenting with respiratory distress due to choanal atresia or lung hypoplasia, requiring immediate evaluation and management.

Billing Considerations

Consideration must be given to the age of the patient and the timing of diagnosis, as some conditions may not be apparent until later in infancy.

Genetics

Documentation Requirements

Genetic documentation should include family history, genetic testing results, and any syndromic associations with congenital lung malformations.

Common Clinical Scenarios

Scenarios may involve genetic counseling for families with a history of congenital malformations or syndromes that include respiratory anomalies.

Billing Considerations

Genetic coders must be aware of the potential for chromosomal abnormalities that may co-occur with lung malformations, impacting coding decisions.

Coding Guidelines

Inclusion Criteria

Use Q33.8 When
  • Official coding guidelines for congenital conditions emphasize the importance of specificity in documentation, including the type of malformation and any associated conditions
  • Coders should refer to the ICD
  • CM Official Guidelines for Coding and Reporting for detailed instructions

Exclusion Criteria

Do NOT use Q33.8 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

39501CPT Code

Repair of tracheoesophageal fistula

Clinical Scenario

Used in cases where surgical intervention is required for tracheoesophageal fistula.

Documentation Requirements

Detailed operative report and pre-operative assessment.

Specialty Considerations

Pediatric surgeons must document the specific type of fistula and any associated anomalies.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for greater specificity in coding congenital malformations, improving the ability to capture the complexity of these conditions and their management.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for greater specificity in coding congenital malformations, improving the ability to capture the complexity of these conditions and their management.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for greater specificity in coding congenital malformations, improving the ability to capture the complexity of these conditions and their management.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What documentation is required for coding Q33.8?

Documentation must include a clear description of the congenital malformation, any associated conditions, and the clinical management plan. Surgical reports and imaging studies should also be included to support the diagnosis.