Congenital absence, atresia and stenosis of jejunum
ICD-10 Q41.1 is a billable code used to indicate a diagnosis of congenital absence, atresia and stenosis of jejunum.
Congenital absence, atresia, and stenosis of the jejunum are serious congenital malformations of the digestive system that can significantly impact a child's health and development. These conditions result from improper development of the jejunum during fetal growth, leading to a complete or partial obstruction of the intestinal tract. Symptoms often present shortly after birth and may include bilious vomiting, abdominal distension, and failure to pass meconium. Diagnosis typically involves imaging studies such as X-rays or ultrasounds, which can reveal the absence or narrowing of the jejunum. Surgical intervention is often required to correct these malformations, and the prognosis can vary depending on the severity of the condition and the presence of associated anomalies. Congenital jejunal atresia is frequently associated with other congenital conditions, such as esophageal atresia, Hirschsprung disease, and gastroschisis, necessitating comprehensive evaluation and management by a multidisciplinary team.
Pediatric documentation must include detailed birth history, clinical findings, and surgical reports. Growth and developmental assessments are also crucial.
Common scenarios include newborns presenting with bilious vomiting and abdominal distension, requiring immediate surgical evaluation.
Coders should be aware of the potential for multiple congenital anomalies and ensure comprehensive documentation to support coding.
Genetic documentation should include family history, genetic testing results, and any syndromic associations with congenital conditions.
Scenarios may involve genetic counseling for families with a history of congenital malformations or syndromes associated with jejunal atresia.
Consideration of chromosomal abnormalities that may co-occur with congenital digestive system malformations is essential for accurate coding.
Used in cases of jejunal atresia requiring surgical intervention.
Operative reports detailing the procedure and findings.
Pediatric surgeons must provide comprehensive documentation to support the complexity of the procedure.
Jejunal atresia is often associated with other congenital malformations such as esophageal atresia, Hirschsprung disease, and gastroschisis. Comprehensive evaluation is necessary to identify these conditions.
