Doubling of uterus with doubling of cervix and vagina
ICD-10 Q51.1 is a billable code used to indicate a diagnosis of doubling of uterus with doubling of cervix and vagina.
Doubling of the uterus, cervix, and vagina is a rare congenital malformation characterized by the presence of two uteri, two cervices, and two vaginas. This condition arises from abnormal development during embryogenesis, specifically during the fusion of the Müllerian ducts, which typically form the female reproductive tract. The presence of this duplication can lead to various clinical implications, including complications during pregnancy, menstrual irregularities, and potential challenges in reproductive health. Patients may present with symptoms such as pelvic pain, abnormal bleeding, or difficulties in conception. Diagnosis is often made through imaging studies such as ultrasound or MRI, which can visualize the anatomical anomalies. Management may involve a multidisciplinary approach, including gynecological, obstetric, and sometimes surgical interventions, depending on the severity of the condition and associated symptoms.
Pediatric documentation should include growth and development assessments, family history of congenital anomalies, and any associated symptoms or complications.
Common scenarios include evaluation of newborns with ambiguous genitalia or referral for further assessment of congenital anomalies detected during routine examinations.
Accurate coding requires careful attention to the patient's age, developmental milestones, and any interventions performed.
Genetic documentation should include family history, genetic testing results, and any syndromic associations with the congenital condition.
Genetic counseling sessions for families with a history of congenital malformations or when a child presents with multiple anomalies.
Consideration of chromosomal abnormalities that may coexist with congenital malformations is crucial for accurate coding.
Performed in cases of severe uterine malformations causing significant symptoms.
Operative report detailing the procedure and indications for surgery.
Gynecological specialists should ensure accurate coding based on the surgical findings.
A double uterus can lead to complications such as preterm labor, miscarriage, and abnormal fetal positioning. Close monitoring during pregnancy is essential to manage these risks.
