Doubling of uterus with doubling of cervix and vagina without obstruction
ICD-10 Q51.10 is a billable code used to indicate a diagnosis of doubling of uterus with doubling of cervix and vagina without obstruction.
Doubling of the uterus, cervix, and vagina, also known as uterine didelphys, is a rare congenital malformation resulting from abnormal embryonic development during the early stages of pregnancy. This condition occurs when the Müllerian ducts, which are responsible for forming the female reproductive tract, fail to fuse properly. As a result, the individual may have two separate uterine cavities, each with its own cervix and, in some cases, a duplicated vagina. While many individuals with this condition may remain asymptomatic, some may experience complications such as menstrual irregularities, reproductive challenges, or increased risk of miscarriage. Diagnosis is typically made through imaging studies such as ultrasound or MRI, which can visualize the anatomical structures. Management may involve monitoring and addressing any associated reproductive health issues, but surgical intervention is rarely necessary unless complications arise.
Pediatric documentation should include growth and development assessments, any associated anomalies, and detailed descriptions of symptoms or complications.
Common scenarios include evaluation of a newborn with ambiguous genitalia or a child presenting with recurrent urinary tract infections.
Consideration of the psychosocial impact on the patient and family, as well as the need for multidisciplinary care.
Genetic documentation should include family history, genetic testing results, and any syndromic associations.
Scenarios may involve genetic counseling for families with a history of congenital malformations or chromosomal abnormalities.
Awareness of potential genetic syndromes associated with uterine malformations, such as Turner syndrome.
May be performed if complications arise from uterine didelphys.
Document indications for surgery and any associated findings.
Considerations for reproductive health and future pregnancies.
Women with a didelphys uterus can have successful pregnancies, but they may face increased risks such as preterm labor, miscarriage, and malpresentation. Close monitoring and individualized care are essential.
