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v1.0.0
ICD-10 Guide
ICD-10 CodesQ61.4

Q61.4

Billable

Renal dysplasia

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q61.4 is a billable code used to indicate a diagnosis of renal dysplasia.

Key Diagnostic Point:

Renal dysplasia is a congenital malformation characterized by the abnormal development of the kidneys, leading to structural and functional impairments. This condition can manifest as a solitary kidney or bilateral involvement, often associated with other urinary tract anomalies. Renal dysplasia may present with varying degrees of severity, from mild dysfunction to complete renal failure, depending on the extent of the developmental disruption. It is frequently linked to other congenital anomalies, including renal agenesis, where one or both kidneys fail to develop, and polycystic kidney disease, where cysts form within the renal tissue. The condition can also be associated with bladder exstrophy and posterior urethral valves, which complicate urinary function and may require surgical intervention. Diagnosis typically involves imaging studies such as ultrasound or MRI, alongside clinical evaluation. Management strategies may include monitoring renal function, addressing associated anomalies, and preparing for potential renal replacement therapy in severe cases.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and severity of renal dysplasia
  • Association with multiple congenital anomalies
  • Need for comprehensive documentation of associated conditions
  • Potential for evolving treatment plans based on renal function

Audit Risk Factors

  • Inadequate documentation of associated congenital anomalies
  • Failure to specify the severity of renal dysplasia
  • Misclassification with similar renal conditions
  • Lack of follow-up documentation on renal function

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Detailed pediatric history, including prenatal factors and family history of congenital conditions.

Common Clinical Scenarios

Infants presenting with failure to thrive, recurrent urinary tract infections, or hypertension due to renal dysplasia.

Billing Considerations

Pediatric coders must ensure accurate coding of associated anomalies and monitor for changes in renal function over time.

Genetics

Documentation Requirements

Genetic testing results, family pedigree, and documentation of any syndromic associations.

Common Clinical Scenarios

Cases where renal dysplasia is part of a genetic syndrome, requiring genetic counseling and testing.

Billing Considerations

Genetic coders should focus on the implications of chromosomal abnormalities that may contribute to renal dysplasia.

Coding Guidelines

Inclusion Criteria

Use Q61.4 When
  • Follow ICD
  • CM guidelines for coding congenital conditions, ensuring specificity in documentation and coding for associated anomalies
  • Use additional codes to capture related conditions when applicable

Exclusion Criteria

Do NOT use Q61.4 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

50360CPT Code

Kidney transplant

Clinical Scenario

Used in cases of end-stage renal disease due to renal dysplasia.

Documentation Requirements

Document the indication for transplant and any prior interventions.

Specialty Considerations

Nephrology and transplant surgery documentation must align with coding.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for greater specificity in coding congenital conditions, improving the accuracy of data collection and reimbursement processes for renal dysplasia and related anomalies.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for greater specificity in coding congenital conditions, improving the accuracy of data collection and reimbursement processes for renal dysplasia and related anomalies.

Reimbursement & Billing Impact

reimbursement processes for renal dysplasia and related anomalies.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What is the difference between renal dysplasia and renal agenesis?

Renal dysplasia refers to abnormal kidney development, which may result in structural anomalies and impaired function, while renal agenesis is the complete absence of one or both kidneys. Accurate coding requires distinguishing between these conditions based on clinical findings and imaging results.