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ICD-10 Guide
ICD-10 CodesQ63.1

Q63.1

Billable

Lobulated, fused and horseshoe kidney

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q63.1 is a billable code used to indicate a diagnosis of lobulated, fused and horseshoe kidney.

Key Diagnostic Point:

Lobulated, fused, and horseshoe kidney are congenital malformations of the kidneys characterized by abnormal kidney shape and position. A horseshoe kidney occurs when the two kidneys are fused together at their lower ends, forming a U-shape. This condition can lead to various complications, including urinary obstruction, hydronephrosis, and increased risk of urinary tract infections. Lobulated kidneys may present with multiple lobes or segments, which can also affect renal function. These anomalies are often detected through imaging studies such as ultrasound or CT scans during prenatal or postnatal evaluations. The exact etiology is not fully understood, but genetic factors and environmental influences during fetal development are believed to play a role. Patients with these conditions may require ongoing monitoring and management to address potential complications and ensure optimal renal function.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and severity of renal anomalies
  • Need for detailed imaging reports to confirm diagnosis
  • Potential for associated urinary tract anomalies
  • Differentiation from other renal malformations

Audit Risk Factors

  • Inadequate documentation of imaging findings
  • Failure to document associated urinary tract anomalies
  • Misclassification of renal malformations
  • Lack of follow-up documentation on renal function

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Pediatric documentation should include growth parameters, developmental milestones, and specific renal function tests.

Common Clinical Scenarios

Common scenarios include prenatal diagnosis via ultrasound, postnatal evaluation of renal function, and management of urinary tract infections.

Billing Considerations

Considerations include the age of the patient, potential for surgical intervention, and long-term follow-up for renal health.

Genetics

Documentation Requirements

Genetic documentation should include family history, genetic testing results, and any syndromic associations.

Common Clinical Scenarios

Scenarios may involve genetic counseling for families with a history of congenital kidney malformations and evaluation for syndromic conditions.

Billing Considerations

Considerations include the potential for chromosomal abnormalities and the need for multidisciplinary management.

Coding Guidelines

Inclusion Criteria

Use Q63.1 When
  • Follow official ICD
  • CM guidelines for coding congenital conditions, ensuring accurate documentation of the diagnosis, associated conditions, and any complications

Exclusion Criteria

Do NOT use Q63.1 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

50360CPT Code

Nephrectomy, partial

Clinical Scenario

Used in cases of severe obstruction or complications from horseshoe kidney.

Documentation Requirements

Document indications for surgery, imaging findings, and preoperative assessments.

Specialty Considerations

Urology specialists should provide detailed operative reports.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of congenital conditions, improving the accuracy of data collection and reimbursement processes. Q63.1 provides a clear classification for lobulated, fused, and horseshoe kidneys, facilitating better tracking of these conditions.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of congenital conditions, improving the accuracy of data collection and reimbursement processes. Q63.1 provides a clear classification for lobulated, fused, and horseshoe kidneys, facilitating better tracking of these conditions.

Reimbursement & Billing Impact

reimbursement processes. Q63.1 provides a clear classification for lobulated, fused, and horseshoe kidneys, facilitating better tracking of these conditions.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What are the common complications associated with horseshoe kidney?

Common complications include urinary obstruction, hydronephrosis, recurrent urinary tract infections, and hypertension. Regular monitoring and management are essential to address these issues.