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ICD-10 Guide
ICD-10 CodesQ64.2

Q64.2

Billable

Congenital posterior urethral valves

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q64.2 is a billable code used to indicate a diagnosis of congenital posterior urethral valves.

Key Diagnostic Point:

Congenital posterior urethral valves (PUV) are a significant cause of urinary obstruction in male infants, characterized by the presence of abnormal flaps of tissue in the posterior urethra. These valves can obstruct urine flow from the bladder, leading to a range of complications including hydronephrosis, renal damage, and bladder dysfunction. The condition is often diagnosed prenatally via ultrasound, where signs such as dilated renal pelvis and bladder distension may be observed. Postnatally, symptoms may include poor urinary stream, urinary tract infections, and failure to thrive. Management typically involves surgical intervention to remove the valves, which can significantly improve urinary function and renal outcomes. Long-term follow-up is essential, as patients may develop complications such as bladder dysfunction or recurrent urinary tract infections. The condition is part of a broader category of congenital malformations affecting the urinary system, including renal agenesis, polycystic kidney disease, and bladder exstrophy, each presenting unique challenges in diagnosis and management.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in clinical presentation and severity of symptoms.
  • Need for precise documentation of urinary tract imaging findings.
  • Potential for associated anomalies requiring additional coding.
  • Differentiation from other urinary tract obstructions.

Audit Risk Factors

  • Inadequate documentation of surgical procedures.
  • Failure to capture associated congenital anomalies.
  • Misclassification of urinary obstruction severity.
  • Lack of follow-up documentation on renal function.

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Detailed clinical notes on urinary symptoms, imaging results, and surgical interventions.

Common Clinical Scenarios

Infants presenting with urinary obstruction, prenatal diagnosis of PUV, and post-surgical follow-up.

Billing Considerations

Consideration of associated anomalies and long-term renal function monitoring.

Genetics

Documentation Requirements

Genetic counseling notes, family history, and any chromosomal analysis results.

Common Clinical Scenarios

Assessment of genetic syndromes associated with urinary malformations.

Billing Considerations

Awareness of potential chromosomal abnormalities that may co-occur with PUV.

Coding Guidelines

Inclusion Criteria

Use Q64.2 When
  • Follow ICD
  • CM guidelines for congenital conditions, ensuring accurate documentation of the diagnosis, associated anomalies, and any surgical procedures performed

Exclusion Criteria

Do NOT use Q64.2 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

52330CPT Code

Cystoscopy with fulguration of posterior urethral valves

Clinical Scenario

Used during surgical intervention for PUV.

Documentation Requirements

Document indication for procedure and findings during cystoscopy.

Specialty Considerations

Urology specialists should ensure accurate coding of surgical interventions.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of congenital conditions like PUV, improving the accuracy of data collection and reimbursement processes.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of congenital conditions like PUV, improving the accuracy of data collection and reimbursement processes.

Reimbursement & Billing Impact

reimbursement processes.

Resources

Clinical References

  • •
    American Urological Association Guidelines

Coding & Billing References

  • •
    American Urological Association Guidelines

Frequently Asked Questions

What are the common complications associated with congenital posterior urethral valves?

Common complications include hydronephrosis, recurrent urinary tract infections, and bladder dysfunction. Long-term follow-up is essential to monitor renal function and manage any arising issues.