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v1.0.0
ICD-10 Guide
ICD-10 CodesQ64.8

Q64.8

Billable

Other specified congenital malformations of urinary system

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q64.8 is a billable code used to indicate a diagnosis of other specified congenital malformations of urinary system.

Key Diagnostic Point:

Congenital malformations of the urinary system encompass a variety of conditions that can significantly impact renal function and urinary tract anatomy. Renal agenesis, characterized by the absence of one or both kidneys, can lead to severe complications, including hypertension and renal failure. Polycystic kidney disease, a genetic disorder, results in the formation of numerous cysts in the kidneys, leading to enlarged kidneys and potential renal dysfunction. Bladder exstrophy is a rare condition where the bladder is formed outside the body, requiring surgical intervention for proper urinary function and cosmetic appearance. Posterior urethral valves, a condition primarily affecting males, involve the presence of abnormal flaps of tissue in the urethra, obstructing urine flow and potentially causing bladder and kidney damage. Accurate coding of these conditions is crucial for appropriate management and treatment planning.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and severity of conditions
  • Need for detailed clinical documentation to support coding
  • Potential for multiple congenital anomalies complicating diagnosis
  • Differentiation between similar conditions requiring precise coding

Audit Risk Factors

  • Inadequate documentation of the specific congenital condition
  • Failure to capture associated anomalies
  • Misclassification of conditions with similar presentations
  • Lack of clarity in the clinical narrative

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Pediatric documentation should include detailed birth history, prenatal exposures, and family history of congenital conditions.

Common Clinical Scenarios

Common scenarios include newborns presenting with renal agenesis or bladder exstrophy, requiring immediate surgical intervention and long-term follow-up.

Billing Considerations

Consideration must be given to the developmental impact of urinary malformations on growth and psychosocial aspects in pediatric patients.

Genetics

Documentation Requirements

Genetic documentation should include family pedigree, genetic testing results, and any syndromic associations with urinary malformations.

Common Clinical Scenarios

Scenarios may involve genetic counseling for families with a history of polycystic kidney disease or congenital urinary tract anomalies.

Billing Considerations

Genetic implications of congenital urinary malformations should be documented, especially in cases with known hereditary patterns.

Coding Guidelines

Inclusion Criteria

Use Q64.8 When
  • Follow official ICD
  • CM guidelines for coding congenital conditions, ensuring specificity and accuracy in documentation
  • Conditions should be coded based on the most definitive diagnosis available

Exclusion Criteria

Do NOT use Q64.8 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

50590CPT Code

Laparoscopic nephrectomy

Clinical Scenario

Used in cases of renal agenesis with complications.

Documentation Requirements

Document indication for nephrectomy and any associated findings.

Specialty Considerations

Pediatric surgeons may have specific protocols for documenting congenital cases.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for greater specificity in coding congenital conditions, improving data accuracy and facilitating better patient management.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for greater specificity in coding congenital conditions, improving data accuracy and facilitating better patient management.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for greater specificity in coding congenital conditions, improving data accuracy and facilitating better patient management.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What documentation is required for coding Q64.8?

Documentation must include a clear diagnosis of the specific congenital malformation, any associated anomalies, and the clinical rationale for the diagnosis. Detailed clinical notes and imaging results are essential for accurate coding.