Other specified congenital malformations of urinary system
ICD-10 Q64.8 is a billable code used to indicate a diagnosis of other specified congenital malformations of urinary system.
Congenital malformations of the urinary system encompass a variety of conditions that can significantly impact renal function and urinary tract anatomy. Renal agenesis, characterized by the absence of one or both kidneys, can lead to severe complications, including hypertension and renal failure. Polycystic kidney disease, a genetic disorder, results in the formation of numerous cysts in the kidneys, leading to enlarged kidneys and potential renal dysfunction. Bladder exstrophy is a rare condition where the bladder is formed outside the body, requiring surgical intervention for proper urinary function and cosmetic appearance. Posterior urethral valves, a condition primarily affecting males, involve the presence of abnormal flaps of tissue in the urethra, obstructing urine flow and potentially causing bladder and kidney damage. Accurate coding of these conditions is crucial for appropriate management and treatment planning.
Pediatric documentation should include detailed birth history, prenatal exposures, and family history of congenital conditions.
Common scenarios include newborns presenting with renal agenesis or bladder exstrophy, requiring immediate surgical intervention and long-term follow-up.
Consideration must be given to the developmental impact of urinary malformations on growth and psychosocial aspects in pediatric patients.
Genetic documentation should include family pedigree, genetic testing results, and any syndromic associations with urinary malformations.
Scenarios may involve genetic counseling for families with a history of polycystic kidney disease or congenital urinary tract anomalies.
Genetic implications of congenital urinary malformations should be documented, especially in cases with known hereditary patterns.
Used in cases of renal agenesis with complications.
Document indication for nephrectomy and any associated findings.
Pediatric surgeons may have specific protocols for documenting congenital cases.
Documentation must include a clear diagnosis of the specific congenital malformation, any associated anomalies, and the clinical rationale for the diagnosis. Detailed clinical notes and imaging results are essential for accurate coding.