Lobster-claw hand, bilateral
ICD-10 Q71.63 is a billable code used to indicate a diagnosis of lobster-claw hand, bilateral.
Lobster-claw hand, also known as split hand/split foot malformation, is a congenital condition characterized by the absence of one or more central digits of the hand, resulting in a claw-like appearance. In bilateral cases, both hands exhibit this deformity. The condition is often associated with other congenital anomalies and can be part of syndromic presentations such as Ectrodactyly-Ectodermal Dysplasia-Clefting (EEC) syndrome. The pathophysiology involves disruptions in the development of the limb bud during embryogenesis, leading to the failure of proper digit formation. Clinical evaluation typically includes a thorough physical examination, family history assessment, and may involve genetic testing to identify associated syndromes. Management may require surgical intervention for functional improvement and cosmetic correction, alongside occupational therapy to enhance hand function. Early intervention is crucial for optimal outcomes in affected children.
Detailed physical examination findings, family history, and any associated conditions.
Assessment of newborns with limb deformities, follow-up visits for surgical interventions, and therapy sessions.
Ensure accurate representation of the bilateral nature and any functional limitations in documentation.
Genetic testing results, family pedigree, and any syndromic associations.
Genetic counseling sessions for families, diagnosis of syndromic conditions, and discussions regarding recurrence risks.
Document any genetic syndromes associated with lobster-claw hand to ensure comprehensive coding.
Used during surgical correction of lobster-claw hand to improve function.
Document the surgical procedure, indications, and any grafting performed.
Ensure that the surgical approach aligns with pediatric standards for limb reconstruction.
Coding lobster-claw hand as bilateral is crucial for accurate representation of the patient's condition, which impacts treatment planning, surgical interventions, and potential genetic counseling for the family.
