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ICD-10 Guide
DiagnosesAnca Vasculitis

Anca Vasculitis

ICD-10 Coding for ANCA Vasculitis(I77.82)

PRIMARY SPECIALTYNephrology
COMPLEXITYHigh
LAST UPDATED09/08/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Anca Vasculitis?
Essential facts and insights about ANCA Vasculitis

Key Clinical Considerations:

  • Presence of anti-neutrophil cytoplasmic antibodies (ANCA) in blood tests
  • Signs of systemic vasculitis such as fever, fatigue, weight loss, and muscle and joint pain
  • Kidney involvement demonstrated by proteinuria, hematuria, or renal insufficiency
  • Evidence of vasculitis in biopsy of affected organ

Clinical Information

Clinical Criteria & Documentation Requirements

  • Detailed documentation of clinical signs and symptoms
  • Results of laboratory tests, especially ANCA levels
  • Evidence of organ involvement, particularly the kidneys
  • Histopathological findings if a biopsy has been performed

Coding Guidelines

Usage Guidelines & Examples

  • I77.82 is specific for ANCA Vasculitis. It should not be confused with codes for other forms of vasculitis
  • Distinguish from I77.6 (Arteritis, unspecified) which is a more general code for any type of arteritis

Code Exclusions

Important Exclusions

  • Other types of vasculitis such as Giant Cell Arteritis or Takayasu Arteritis
  • Conditions where ANCA test is positive but no signs of vasculitis

Related ICD-10 Codes

Primary Codes
I77.82
Embolism and thrombosis of artery of unspecified site
Ancillary Codes
N18.x
J84.89
Differential Codes
I77.6
M31.7

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Nephrology

Specialty Applications

  • Patients with confirmed diagnosis of ANCA Vasculitis
  • Scenarios where there is systemic vasculitis with positive ANCA test

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Template 1

Patient presents with systemic vasculitis and positive ANCA test, confirming diagnosis of ANCA Vasculitis.

Template 2

ANCA Vasculitis diagnosis supported by clinical symptoms, positive ANCA test, and kidney involvement.

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

What is the key diagnostic criterion for ANCA Vasculitis?

The presence of anti-neutrophil cytoplasmic antibodies (ANCA) in blood along with signs of systemic vasculitis.

When should this code be used?

This code should be used when a confirmed diagnosis of ANCA Vasculitis has been made.