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v1.0.0
ICD-10 Guide
DiagnosesAutoimmune Hemolytic Anemia

Autoimmune Hemolytic Anemia

ICD-10 Coding for Autoimmune Hemolytic Anemia(D59.11, D59.12, D59.13, D59.10)

PRIMARY SPECIALTYHematology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Autoimmune Hemolytic Anemia?
Essential facts and insights about Autoimmune Hemolytic Anemia

Key Clinical Considerations:

  • Fatigue, pallor, jaundice, dark urine
  • Positive direct Coombs test, elevated reticulocyte count, low hemoglobin
  • Splenomegaly, signs of hemolysis on physical exam

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history, clinical findings, lab results
  • ICD-10 terminology: Autoimmune hemolytic anemia (D59.1)
  • Example: 'Patient presents with fatigue and jaundice, direct Coombs test positive.'

Coding Guidelines

Usage Guidelines & Examples

  • Follow guidelines for specificity in coding autoimmune conditions.
  • Common errors include misclassifying hemolytic anemia types.

Code Exclusions

Important Exclusions

  • Thalassemia, sickle cell anemia
  • D59.0 - Non-autoimmune hemolytic anemia

Related ICD-10 Codes

Primary Codes
D59.1
Autoimmune hemolytic anemia
Ancillary Codes
R16.1
D64.9
Differential Codes
D59.12
D59.11

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Hematology

Specialty Applications

  • Adults and children with autoimmune disorders
  • Hematology clinics, outpatient settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

Documentation requirements?

Include patient history, lab results, and clinical findings.

Billing considerations?

Ensure accurate coding to reflect the diagnosis and any related treatments.